1

 

                DEPARTMENT OF HEALTH AND HUMAN SERVICES

 

                      FOOD AND DRUG ADMINISTRATION

 

                CENTER FOR DRUG EVALUATION AND RESEARCH

 

 

                    PEDIATRIC ADVISORY SUBCOMMITTEE

 

             OF THE ANTI-INFECTIVE DRUGS ADVISORY COMMITTEE

 

 

 

 

 

 

                        Wednesday, June 9, 2004

 

                               8:00 a.m.

 

 

                          ACS Conference Room

                               Room 1066

                           5630 Fishers Lane

                          Rockville, Maryland

                                                                 2

 

                              PARTICIPANTS

 

         Joan P. Chesney, M.D., Chair

         Thomas H. Perez, M.P.H., Executive Secretary

      CONSULTANTS (VOTING):

 

         Mark Hudak, M.D.

         David Danford, M.D.

         Richard Gorman, M.D.

         Robert Nelson, M.D., Ph.D.

         Susan Fuchs, M.D.

         Victor Santana, M.D.

         Naomi Luban, M.D.

         Judith O'Fallon, Ph.D.

         Katherine L. Wisner, M.D.

 

      MEMBER OF THE ANTI-INFECTIVE DRUGS ADVISORY

      COMMITTEE (VOTING):

 

         Steve Ebert, Pharm.D., Consumer Representative

 

         FEDERAL GOVERNMENT EMPLOYEE (VOTING):

 

         Janet Cragan, M.D.

 

         INDUSTRY REPRESENTATIVE TO ANTI-INFECTIVE DRUGS

         ADVISORY COMMITTEE (NON-VOTING):

 

         Sam Maldonado, M.D., industry representative

 

      FDA STAFF:

 

         Solomon Iyasu, M.D.

         Susan Cummins, M.D.

         Shirley Murphy, M.D.

         Dianne Murphy, M.D.

                                                                 3

 

                            C O N T E N T S

 

      Call to Order and Introductions,

         Joan P. Chesney, M.D.                                   5

 

      Meeting Statement, Thomas H. Perez, M.P.H.                 7

 

      Welcome, Dianne Murphy, M.D.                              10

 

      Adverse Event Reports per Section 17 of Best

         Pharmaceutical for Children Act,

         Solomon Iyasu, M.D.                                    15

 

         Fexofenodine, Jane Filie, M.D.                         22

 

         Topotecan and Temozolomide, Susan McCune, M.D.         34

 

         Moxifloxacin and Ciprofloxacin,

            Harry Gunkel, M.D.                                  59

 

         Fosinopril, Larry Grylack, M.D.                        66

 

         Fentanyl, ShaAvhree Buckman, M.D.                      78

         David J. Lee, Ph.D.                                    89

         D. Elizabeth McNeil, M.D.                              91

 

      Discussion of Question 1                                  92

 

      Adverse Event Reports per Section 17 of BPCA

      (cont.), Venlafaxine, Hari Sachs, M.D.                   115

 

      Pediatric Update, Dianne Murphy, M.D.                    148

 

      Meeting Statement, Thomas H. Perez, M.P.H.               170

 

      Update on Neonatal Withdrawal Syndrome:

 

         Kathleen Phelan, R.Ph.                                174

         Robert Levin, M.D.                                    189

         Katherine Wisner, M.D.,

           Women's Behavioral Health CARE                      216

 

      Discussion of Questions 2 and 3                          254

 

      Update on Congenital Eye Malformations in Infants,

         Solomon Iyasu, M.D.                                   303

                                                                 4

 

                      C O N T E N T S (Continued)

 

      Open Public Hearing:

 

         Philip Sanford Zeskind, Ph.D., University

            of North Carolina                                  309

 

      Pediatric Research Equity Act,

         Shirley Murphy, M.D.                                  326

 

      Overview of Institute of Medicine Report, "Ethical

         Conduct of Clinical Research Involving

         Children," Robert Nelson, M.D.                        340

 

                                                                 5

 

  1                      P R O C E E D I N G S

 

  2                   Call to Order, Introductions

 

  3             DR. CHESNEY:  Good morning.  I think we

 

  4   are ready to get started.  I would like to welcome

 

  5   everybody to this meeting which, for those in the

 

  6   room who don't know, and Dr. Murphy will elaborate

 

  7   on this, this is the last meeting for this group of

 

  8   the Pediatric Subcommittee as currently

 

  9   constituted.  I would like to also mention that Dr.

 

 10   Mimi Glode will not be with us because her father

 

 11   became ill on Sunday and she had to cancel at the

 

 12   last minute.

 

 13             Tom has just told me that traffic is going

 

 14   to become very bad this afternoon because of

 

 15   President Reagan's funeral so we want to keep that

 

 16   in mind as we move on throughout the day.  So, I

 

 17   think we will start with introductions and, Dr.

 

 18   Maldonado, would you like to start?

 

 19             DR. MALDONADO:  Sam Maldonado, from

 

 20   Johnson & Johnson, the industry representative on

 

 21   this committee.

 

 22             DR. FUCHS:  Susan Fuchs, pediatric

 

                                                                 6

 

  1   emergency medicine physician from Children's

 

  2   Memorial Hospital in Chicago.

 

  3             DR. O'FALLON:  Judith O'Fallon,

 

  4   statistics, retired from the Mayo Clinic.

 

  5             DR. SANTANA:  Victor Santana, pediatric

 

  6   hematologist/oncologist from St. Jude's Children's

 

  7   Research Hospital in Memphis, Tennessee.

 

  8             DR. GORMAN:  Rich Gorman, pediatric

 

  9   private practice in Ellicott City, Maryland.

 

 10             DR. EBERT:  Steve Ebert, pharmacist,

 

 11   infectious diseases, Meriter Hospital and

 

 12   University of Wisconsin, Madison.

 

 13             DR. PEREZ:  Tom Perez, executive secretary

 

 14   to this committee meeting.

 

 15             DR. CHESNEY:  Joan Chesney, pediatric

 

 16   infectious disease at the University of Tennessee

 

 17   in Memphis, and also St. Jude's Children's Research

 

 18   Hospital.

 

 19             DR. HUDAK:  Mark Hudak, neonatologist,

 

 20   University of Florida, Jacksonville.

 

 21             DR. DANFORD:  Dave Danford, pediatric

 

 22   cardiology, University of Nebraska Medical Center,

 

                                                                 7

 

  1   Omaha.

 

  2             DR. NELSON:  Robert Nelson, pediatric

 

  3   critical care medicine, Children's Hospital,

 

  4   Philadelphia and University of Pennsylvania.

 

  5             DR. IYASU:  Solomon Iyasu, lead medical

 

  6   officer in pediatrics, FDA.

 

  7             DR. CUMMINS:  Susan Cummins, lead medical

 

  8   officer, pediatrics, FDA.

 

  9             DR. S. MURPHY:  Shirley Murphy, Division

 

 10   Director, Division of Pediatric Drug Development,

 

 11   FDA.

 

 12             DR. D. MURPHY:  Dianne Murphy, Office

 

 13   Director, Office of Counter-terrorism and Pediatric

 

 14   Drug Development, in the Office of Pediatric

 

 15   Therapeutics.

 

 16             DR. CHESNEY:  Thank you.  Now Tom Perez

 

 17   will read the meeting statement.

 

 18                        Meeting Statement

 

 19             DR. PEREZ:  Thank you and good morning.

 

 20   The following announcement addresses the issue of

 

 21   conflict of interest with regard to the adverse

 

 22   event reporting session and is made part of the

 

                                                                 8

 

  1   record to preclude even the appearance of such at

 

  2   this meeting.

 

  3             Based on the submitted agenda for the

 

  4   meeting and all financial interests reported by the

 

  5   committee participants, it has been determined that

 

  6   all interests in firms regulated by the Center for

 

  7   Drug Evaluation and Research present no potential

 

  8   for an appearance of a conflict of interest at this

 

  9   meeting, with the following exceptions:

 

 10             In accordance with 18 USC 208(b)(3), full

 

 11   waivers have been granted to the following

 

 12   participants, Dr. Richard Gorman for ownership of

 

 13   stock in a company with a product at issue, valued

 

 14   between $50,001 to $100,000; Dr. Judith O'Fallon

 

 15   for her and her sponsor's ownership of stock in a

 

 16   company with a product at issue, between $5,001 and

 

 17   $25,000; Dr. Katherine Wisner, for her speaker's

 

 18   bureau activities for a company with a product at

 

 19   issue for which she receives less than $10,001 per

 

 20   year; Dr. Patricia Chesney for her spouse's

 

 21   ownership of stock in a company with a product at

 

 22   issue, valued from $5,001 to $25,000 and unrelated

 

                                                                 9

 

  1   consultant earnings less than $10,001 per year.  In

 

  2   addition, Dr. Chesney's spouse owns stock in a

 

  3   company with a product at issue, worth less than

 

  4   $5,001.  Because this stock interest falls below

 

  5   the minimis exception allowed under 5 CFR

 

  6   2640.202(b)(2), a waiver under 18 USC 208 is not

 

  7   required.  Further, Dr. Chesney is recused from

 

  8   participating from the subcommittee's discussion

 

  9   regarding Duragesic due to a conflict of interest.

 

 10             A copy of the waiver statements may be

 

 11   obtained by submitting a written request to the

 

 12   agency's Freedom of Information Office, Room 12A-30

 

 13   of the Parklawn Building.  In the event that the

 

 14   discussions involve any other products or firms not

 

 15   already on the agenda for which an FDA participant

 

 16   has a financial interest, the participants are

 

 17   aware of the need to exclude themselves from such

 

 18   involvement and their exclusion will be noted for

 

 19   the record.

 

 20             We would also like to note that Dr. Samuel

 

 21   Maldonado has been invited to participate as an

 

 22   industry representative, acting on behalf of

 

                                                                10

 

  1   regulated industry.  Dr. Maldonado is employed by

 

  2   Johnson & Johnson.  With respect to all other

 

  3   participants, we ask in the interest of fairness

 

  4   that they address any current or previous financial

 

  5   involvement with any firm whose product they may

 

  6   wish to comment upon.  Thank you.

 

  7             DR. CHESNEY:  Thank you.  Our first

 

  8   speaker for the morning will be Dr. Dianne Murphy,

 

  9   Director of the Counter-terrorism and Pediatric

 

 10   Drug Development Office.

 

 11                             Welcome

 

 12             DR. D. MURPHY:  And just as you all

 

 13   understand how those two got to be combined, we

 

 14   have come to the end of an era.  That was really

 

 15   the substance of my opening comments this morning

 

 16   and I am going to talk more about this later in the

 

 17   day, that this is a milestone.

 

 18             But I wanted to take this morning to focus

 

 19   on the importance of the activity of this committee

 

 20   in the review of the safety or adverse events that

 

 21   occur after a product has been granted exclusivity.

 

 22   It has been clearly legislatively mandated that

 

                                                                11

 

  1   this is going to occur and that task has come to

 

  2   this committee.

 

  3             I wanted to make sure that you all

 

  4   realized how much you have contributed to this

 

  5   process.  We have received feedback from you during

 

  6   the time about what was useful and have tried to

 

  7   maintain a course, as we have to, that obeys the

 

  8   legislative intent and, yet, makes it more

 

  9   scientifically interesting within the constraints

 

 10   that we have.  I think probably years from now we

 

 11   could come and ask you all what are the problems

 

 12   with the AERS data reporting system.  So, you have

 

 13   been mandated to participate in a process in which

 

 14   you were told every meeting that you come here that

 

 15   the limitations are numerous with passive

 

 16   reporting; that when we do get reporting it is

 

 17   either poor or limited in nature; that there is

 

 18   little ability to go back and reconstruct in detail

 

 19   any of that information; and it basically doesn't

 

 20   have the same quality as a prospective surveillance

 

 21   or active process.  Yet, during this time I think

 

 22   we have evolved a process, again with your feedback

 

                                                                12

 

  1   and assistance, that has allowed us to make it more

 

  2   valuable.

 

  3             I would like to say that I think that what

 

  4   we have been able to identify over the past year or

 

  5   so has been the benefits of this system, and that

 

  6   is that it ensures that attention is focused on

 

  7   what is happening postmarketing to these products

 

  8   that the government initiates and rewards for

 

  9   studies being conducted.  As most of you are aware,

 

 10   one of the largest safety databases that occurs

 

 11   with any product is the postmarketing activities.

 

 12   That is where you find your rare serious events.

 

 13   And, this process has been critical for this

 

 14   committee and this has been a very important

 

 15   activity that I do think has focused and ensured

 

 16   that products that are marketed for children are

 

 17   looked at in a studied way, a reliable way, a

 

 18   predictable way, and I think that that is

 

 19   important.

 

 20             Now, why is it important?  Because I don't

 

 21   know how many times you have sat through these

 

 22   meetings where we said, "well, here are the

 

                                                                13

 

  1   problems and we didn't see anything.  Okay?"  But

 

  2   that is good news.  We would hope that the majority

 

  3   by far, if not 100 percent of these products that

 

  4   are studied and marketed don't have serious hidden

 

  5   adverse events.  So, in a say, it is like

 

  6   prophylaxis.  We hope we don't find major issues.

 

  7             But I think the other thing that this

 

  8   process has done that I wanted you all to know

 

  9   about that was important is that it has the effect

 

 10   on the agency of re-prioritizing pediatric safety

 

 11   assessments.  As everyone knows, there are many

 

 12   deadlines the agency has to meet and it is hard

 

 13   often to see the plate for all the things that are

 

 14   on it.  But clearly the legislation, your

 

 15   participation and our coming to you says we are

 

 16   having a public meeting and a discussion and it

 

 17   re-prioritizes this activity for the agency, as I

 

 18   said, and ensures that attention occurs.

 

 19             We are going to hear today about some

 

 20   activities that have evolved during this process,

 

 21   some questions that we want to bring to you because

 

 22   of information that, in essence, was moved forward

 

                                                                14

 

  1   a little faster because of this process, not that

 

  2   it was being neglected but because we basically

 

  3   made sure that we facilitated the assessments of

 

  4   some of these products and some of the issues.  In

 

  5   the past, as you know, we have had some reviews of

 

  6   the SSRIs and this whole process has been important

 

  7   in helping facilitate moving that activity forward

 

  8   also.

 

  9             I wanted to just thank you for your

 

 10   scientific input, your thoughtfulness and your

 

 11   feedback which we still would like to receive about

 

 12   the process on adverse event reporting, knowing

 

 13   that we have to work within the constraints of the

 

 14   systems that we presently have.  With that, I will

 

 15   speak a little more about the contributions of this

 

 16   committee and where we are going in the future

 

 17   later today.  Thank you very much.

 

 18             DR. CHESNEY:  Thank you, Dr. Murphy.  Our

 

 19   second speaker this morning, Dr. Solomon Iyasu, is

 

 20   going to talk to us about adverse event reports,

 

 21   per Section 17 of the Best Pharmaceuticals for

 

 22   Children Act.  Dr. Iyasu is a pediatrician, a

 

                                                                15

 

  1   medical epidemiologist who has fellowship training

 

  2   with the EIS of the CDC and residency training in

 

  3   preventive medicine at the CDC.  Prior to joining

 

  4   the FDA, just in 2002, he worked for 13 years as a

 

  5   medical epidemiologist at the CDC, in Atlanta,

 

  6   where he led research and programmatic programs in

 

  7   infant health.  He also served as the CDC liaison

 

  8   to the Committee on the Fetus and Newborn of the

 

  9   American Academy Pediatrics for many years, and has

 

 10   served on several HHS committees and inter-agency

 

 11   working groups, including the National Children's

 

 12   Study.  His research papers have involved maternal

 

 13   and child health issues.  In his current position

 

 14   at the FDA he serves as a medical team leader in

 

 15   the Division of Pediatric Drug Development and also

 

 16   serves as the lead medical officer for safety in

 

 17   the Office of Pediatric Therapeutics, which has

 

 18   become--always was but has become a particularly

 

 19   important office in function.  Dr. Iyasu?

 

 20           Adverse Event Reports per Section 17 of Best

 

 21                 Pharmaceuticals for Children Act

 

 22             DR. IYASU:  Thank you very much, Dr.

 

                                                                16

 

  1   Chesney, for that kind introduction.  Good morning.

 

  2             In the next few minutes I will provide you

 

  3   with an overview of today's agenda.  The theme for

 

  4   today is safety, safety of pediatric drugs.  A

 

  5   series of presentations will discuss postmarketing

 

  6   reviews of adverse events for drugs that have been

 

  7   granted exclusivity.

 

  8             The review of the post exclusivity adverse

 

  9   events is accomplished through the collaboration

 

 10   with the Office of Drug Safety, Office of Pediatric

 

 11   Therapeutics and Division of Pediatric Drug

 

 12   Development.  Therefore, at first I would like to

 

 13   acknowledge the contribution of the staff in the

 

 14   Office of Drug Safety for these reviews.

 

 15             In the morning you will hear adverse event

 

 16   reviews for eight drug products that were granted

 

 17   pediatric exclusivity.  These reviews will be

 

 18   presented by medical officers within the Division

 

 19   of Pediatric Drug Development.  Several of these

 

 20   presentations are informational while a few discuss

 

 21   important issues, ranging from a lack of

 

 22   age-appropriate pediatric formulations for

 

                                                                17

 

  1   fosinopril to a preventable safety signal

 

  2   associated with the use of fentanyl transdermal

 

  3   system or Duragesic.  You will be asked to discuss

 

  4   a question of risk management strategies in

 

  5   relation to fentanyl.  The morning will also

 

  6   include a time for open public hearing, followed by

 

  7   a short pediatric update by Dr. Dianne Murphy.

 

  8             We are doing the adverse event review a

 

  9   little differently than before.  In addition to the

 

 10   usual format which you are familiar with, we have

 

 11   incorporated some of the clinical trial data

 

 12   available in the public domain into these reviews.

 

 13   You are not going to see this component for all the

 

 14   drugs because the trial data are not yet in the

 

 15   public domain for some of the drug products that we

 

 16   will be discussing.

 

 17             This is a pediatric page on the external

 

 18   FDA website where you will find all the publicly

 

 19   available summaries of medical and clinical

 

 20   pharmacology of these pediatric studies for

 

 21   exclusivity.  The process of making these reviews

 

 22   available in the public domain is evolving,

 

                                                                18

 

  1   therefore, some of the reviews that I mentioned

 

  2   before may not be yet available on this website.

 

  3   Nevertheless, I invite you to use it as a resource

 

  4   and urge you to spread the word about this site.

 

  5             In the afternoon we will discuss two

 

  6   pediatric safety issues regarding the use of SSRIs

 

  7   and SNRIs during pregnancy.  As you recall, we

 

  8   discussed several case reports of neonatal

 

  9   withdrawal syndrome related to the use of Paxil and

 

 10   Celexa during the meeting of this committee last

 

 11   February.  At that time you requested more

 

 12   information on the syndrome and FDA's efforts to

 

 13   address it.

 

 14             To address this issue, we have lined up

 

 15   three presentations for you.  Kate Phelan, from the

 

 16   Office of Drug Safety, will present the

 

 17   postmarketing adverse event review for this class

 

 18   of drugs.  Dr. Bob Levin, from the Division of

 

 19   Neuropharmaceutical Drug Products, will speak on

 

 20   the new class labeling regarding neonatal

 

 21   withdrawal toxicity and its rationale.  Dr. Kathy

 

 22   Wisner will address the risk/benefit of treatment

 

                                                                19

 

  1   in child depression, a critical issue for both the

 

  2   practitioner and the patient.  At the end of this

 

  3   update you will be asked to discuss two questions.

 

  4             Next, I will present an update on

 

  5   congenital eye malformations, again, as a fallout

 

  6   to the February meeting when we reported a case

 

  7   report about possible congenital eye malformation

 

  8   related to the use of Celexa during pregnancy.

 

  9   This update will review all postmarketing reports

 

 10   of congenital eye malformations for Celexa and some

 

 11   newer anti-depressants.

 

 12             Before we present the specific adverse

 

 13   events, I will briefly review the data sources used

 

 14   in this review and their limitations.  The Adverse

 

 15   Event Reporting System is a spontaneous and

 

 16   voluntary system.  Because it is a passive system

 

 17   it suffers from a number of limitations, listed

 

 18   here on this slide, that you are already familiar

 

 19   with and we have discussed several times during

 

 20   previous presentations.

 

 21             Again the drug use data source and their

 

 22   limitations have also been presented before and are

 

                                                                20

 

  1   not new to you.  IMS National Prescription Audit

 

  2   Plus is used to estimate the number of outpatient

 

  3   prescriptions but lacks demographic information.

 

  4   The National Disease and Therapeutic Index can

 

  5   estimate drug mentions during office-based

 

  6   physician visits but pediatric use estimates can be

 

  7   unstable for less frequently used medications.

 

  8             Another outpatient data source is the IMS

 

  9   National Sales Perspectives which provides

 

 10   estimates of units sold from manufacturers to

 

 11   various channels of distribution and, therefore,

 

 12   may be a possible surrogate measure for drug use.

 

 13   An important limitation of this data source is

 

 14   absence of demographic information such as age and

 

 15   gender.

 

 16             Important drug use data sources and their

 

 17   limitations are well-known to you.  To refresh your

 

 18   memory, these are described in this slide and the

 

 19   next slide.  The main limitation with all the

 

 20   inpatient data sources, except for Premier, is the

 

 21   inability to make national projections of drug use.

 

 22   However, national estimates from Premier are

 

                                                                21

 

  1   available but are selective.  Furthermore, drug use

 

  2   cannot be linked to diagnosis or procedure and drug

 

  3   use in hospital or outpatient clinics is not

 

  4   captured in this data system.  Data from CHCA are

 

  5   limited to 29 children hospitals and cannot be

 

  6   projected nationally.

 

  7             This concludes my remarks and now let me

 

  8   turn to the presentations for this morning by

 

  9   introducing the first speaker.  But before I do

 

 10   that, I do want to recognize two individuals who

 

 11   have tirelessly worked behind the scenes to make

 

 12   this meeting possible.  Please stand up and be

 

 13   recognized, Miss Christine Phucas and Rosemary

 

 14   Addy.

 

 15             [Applause]

 

 16             Thank you.  Now the next speaker, Dr.

 

 17   Filie is a general pediatrician and pediatric

 

 18   rheumatologist.  She conducted research on

 

 19   molecular biology, connective tissue disorders and

 

 20   genetics at NIH for many years before going into

 

 21   private practice.  She joined the FDA from private

 

 22   practice about a year ago.  She will discuss

 

                                                                22

 

  1   adverse event reports for fexofenodine.  Dr. Filie?

 

  2                           Fexofenodine

 

  3             DR. FILIE:  Good morning, everyone.  I

 

  4   will proceed with the adverse event review for

 

  5   fexofenodine during the one-year post-exclusivity

 

  6   period.

 

  7             Fexofenodine, trade name Allegra, is an

 

  8   antihistamine by Aventis Pharmaceuticals.  The

 

  9   indications for adults and children are relief of

 

 10   symptoms associated with seasonal allergic rhinitis

 

 11   and non-complicated skin manifestations of chronic

 

 12   idiopathic urticaria.  It was originally approved

 

 13   in July, 1996 and pediatric exclusivity was granted

 

 14   in January, 2003.

 

 15             In order to fulfill the requirements for

 

 16   exclusivity, 3 pivotal studies were conducted and

 

 17   415 children, 6 months to 6 years of age, were

 

 18   treated for allergic rhinitis.  One study was a

 

 19   Phase 1 pharmacokinetic study characterizing the

 

 20   dose for children 6 months to 2 years of age.

 

 21   Another study was a Phase 3 study assessing safety

 

 22   and tolerability in 2 groups, 6 months to 2 years

 

                                                                23

 

  1   of age, weighing under 10.5 kg and weighing over

 

  2   10.5 kg.

 

  3             A previous safety and tolerability study

 

  4   on children 2-6 years of age was also submitted.

 

  5   The adverse events occurred at similar frequencies

 

  6   as for placebo, and no new safety signals were

 

  7   observed.

 

  8             Efficacy studies were not conducted due to

 

  9   the fact that the disease course and

 

 10   pathophysiology of allergic rhinitis and chronic

 

 11   idiopathic urticaria, as well as the drug's effect,

 

 12   are similar in children and adult patients.  The

 

 13   studies conducted on children 6 months to 6 years

 

 14   of age utilized fexofenodine powder mixed with

 

 15   apple sauce or rice cereal.  There is no marketable

 

 16   age-appropriate formulation for children 6 months

 

 17   to 6 years of age.

 

 18             Drug use trends for

 

 19   fexofenodine--currently, fexofenodine is the

 

 20   leading prescription for non-sedating antihistamine

 

 21   on the market since loratadine became

 

 22   over-the-counter in 2002.  The total number of

 

                                                                24

 

  1   fexofenodine product dispensed increased from

 

  2   approximately 20.9 million in 2000 to 29.6 million

 

  3   in 2003.  Pediatric patients accounted for

 

  4   approximately 2.5 million prescriptions of

 

  5   fexofenodine dispensed in 2003.  The most common

 

  6   diagnoses associated with the use in pediatric

 

  7   patients in 2003 were allergic rhinitis and

 

  8   allergic disorder.

 

  9             The adverse events from pediatric clinical

 

 10   trials that I just presented are as follows:

 

 11   Headache, accidental injury, cough, fever, pain,

 

 12   otitis media and upper respiratory infection, and

 

 13   least common, insomnia, nervousness, sleep

 

 14   disorders, rashes, urticaria, pruritus and

 

 15   hypersensitivity reactions.

 

 16             During the exclusivity period the total

 

 17   adverse event reports from the AERS database was

 

 18   158, 84 of them in the United States.  Among the

 

 19   158 reports there were 8 unduplicated pediatric

 

 20   reports which included 2 with serious outcomes, 1

 

 21   hospitalization and 1 life-threatening event.

 

 22   There were no pediatric deaths.

 

                                                                25

 

  1             In the 8 pediatric case reports the

 

  2   following unlabeled pediatric adverse events were

 

  3   reported, psychosis exacerbation with suicidal

 

  4   ideation and depression; seizure, visual

 

  5   disturbances; abnormal liver function; fungal

 

  6   urinary tract infection; non-accidental overdose of

 

  7   multiple drugs and prolonged QT, prematurity,

 

  8   maternal experience and medication error.

 

  9             I would like to present you with a

 

 10   synopsis of individual reports.  A 15 year-old with

 

 11   schizoaffective disorder and ADD, on multiple

 

 12   medications, experienced exacerbation of psychosis,

 

 13   suicidal ideation and depression which resolved

 

 14   after discontinuation of fexofenodine.

 

 15             A 13 year-old child presented with grand

 

 16   mal seizures.  The patient was also on multiple

 

 17   medications and one of them was bupropion which has

 

 18   a warning about the potential to cause seizures.

 

 19             A 7 year-old presented transient loss of

 

 20   color vision and visual disturbances such as black

 

 21   dots and bubbles.  It also resolved after

 

 22   discontinuation of the drug in a few days.

 

                                                                26

 

  1             A 10 year-old patient developed a

 

  2   bacterial UTI and abnormal liver function tests

 

  3   after receiving fexofenodine for one week.  The

 

  4   child was on concomitant medications and one of

 

  5   them was labeled for hepatic function impairment.

 

  6   We do not have the name of the drug on the report.

 

  7   The child recovered after discontinuation of

 

  8   fexofenodine.

 

  9             A 16 year-old who developed a fungal UTI

 

 10   and pyelonephritis was hospitalized.  This patient

 

 11   was also on multiple medications for depression and

 

 12   gastritis.

 

 13             A 13 year-old had an intentional overdose

 

 14   of fexofenodine, acetaminophen, metoclopramide and

 

 15   tramadol.  QT prolongation was observed in the

 

 16   emergency room which normalized the following day.

 

 17             The last two cases--a 27-week old

 

 18   premature baby, small for gestational age, was born

 

 19   by C-section due to pre-eclampsia.  There was a

 

 20   history of abnormal alpha-1 fetoprotein.  The

 

 21   mother was on concomitant medications.

 

 22             The last case--a prescription refill was

 

                                                                27

 

  1   mistakenly filled with Zyrtec-D instead of

 

  2   Allegra-D, but no adverse event was reported.

 

  3             Concluding the report, despite the large

 

  4   number of fexofenodine prescriptions, there were

 

  5   few pediatric adverse event reports during the

 

  6   one-year post-pediatric exclusivity period.  It is

 

  7   also very difficult to make any attributions of the

 

  8   adverse events of the drug when there are

 

  9   concomitant medications in the reports.  In this

 

 10   case, the FDA will continue to monitor the adverse

 

 11   event reports in all populations.  Any questions or

 

 12   comments?

 

 13             DR. CHESNEY:  Dr. Santana?

 

 14             DR. SANTANA:  Do you know if there are any

 

 15   similar adult reports with the use of this

 

 16   medication and concomitant anti-psychotic

 

 17   medications in adults?

 

 18             DR. FILIE:  I don't know that I can

 

 19   respond to that adequately.  From the information

 

 20   that we have on the label, the adverse events are

 

 21   very similar in both populations.  They resemble

 

 22   pretty much the two groups.

 

                                                                28

 

  1             DR. S. MURPHY:  Pete Stark I think is here

 

  2   from the Division.  Do you have any comments about

 

  3   adult report?

 

  4             DR. CHESNEY:  Dr. O'Fallon?

 

  5             DR. O'FALLON:  It seems to me that the way

 

  6   you keep your data may help you to find things.

 

  7   So, I am wondering when you have these reports, are

 

  8   you keeping track of the various concomitant

 

  9   medications so that you could be looking for trends

 

 10   developing that may be subtle, that there may be

 

 11   interactions, or something?

 

 12             DR. FILIE:  Yes.  The hope is to

 

 13   accumulate this data over a long time.

 

 14             DR. O'FALLON:  Yes, but I mean in a way so

 

 15   that you are able to go back, search and find those

 

 16   combos?  I am asking about how the data is being

 

 17   collected so that you are going to be able to

 

 18   search on it.

 

 19             DR. FILIE:  Yes, it is possible and we are

 

 20   doing that collecting and the Office of Drug Safety

 

 21   is also involved in this.  This is something that

 

 22   has accumulated and we can keep all this data

 

                                                                29

 

  1   without losing it.

 

  2             DR. O'FALLON:  But in a computer file that

 

  3   you can search?

 

  4             DR. FILIE:  I don't know.

 

  5             DR. IYASU:  Let me respond to this.  The

 

  6   AERS database has been in existence for a long time

 

  7   and the database is searchable both by high risk

 

  8   event terms as well as by the drug name or the

 

  9   trade name.  So, it is searchable by a number of

 

 10   parameters and there is an accumulated database

 

 11   which resides at FDA so you can look at one year or

 

 12   you can look at several years since the first time

 

 13   a report comes into existence for a particular

 

 14   product.  Once there is approval, there are going

 

 15   to be postmarketing reports that come in.  So,

 

 16   there is a way to look at that.  But there isn't a

 

 17   whole lot of information to try to look at multiple

 

 18   permutations of different confounders or looking up

 

 19   interactions.  It is a limited database in that

 

 20   way.

 

 21             DR. D. MURPHY:  I did want to respond that

 

 22   in your package it does tell you that fexofenodine

 

                                                                30

 

  1   has been looked at with the co-administration of

 

  2   acetyl console and erythromycin, the sip

 

  3   interactions.  So, what the agency does is where we

 

  4   know that a metabolism uses a certain sip enzyme

 

  5   that will cause increases or decreases, they will

 

  6   frequently look at that interaction but they can't

 

  7   look at all of them.  That often is actually a

 

  8   negotiated activity as to how many of them they do

 

  9   look at, and whether there are ones that are more

 

 10   likely to give serious adverse events by the normal

 

 11   drugs that might be used with this specific

 

 12   disease.  So, you could see that with an allergic

 

 13   indication you might think that antibiotics would

 

 14   be one of the set of drugs that they would look at.

 

 15             So, I just wanted to put on the table that

 

 16   prospectively the agency will sometimes ask,

 

 17   knowing what the metabolism is, for these

 

 18   interactions.  But, you can imagine that the list

 

 19   could get endless so the agency does not do all

 

 20   possible combinations.  Certainly, I think from

 

 21   allergic rhinitis to antidepressants--I mean,

 

 22   unless you had a mechanistic reason for doing that,

 

                                                                31

 

  1   you wouldn't up front do it.  Your question, I

 

  2   realize, was looking at statistical analysis post

 

  3   but up front there is a certain amount of activity

 

  4   in that area.

 

  5             DR. O'FALLON:  It seems to me that since

 

  6   you only have a handful of reports it might be

 

  7   worth it, that when you see something showing up

 

  8   you would say they took drug A, drug B, drug C,

 

  9   let's look and see if we have any reports in the

 

 10   database, especially in the adults or something, to

 

 11   see if you are seeing if that has been reported

 

 12   before.

 

 13             DR. D. MURPHY:  As noted, ODS has the

 

 14   database and it will have that information in it.

 

 15   So, you could go back and plug in certain drug

 

 16   names.  I think, as always, the caveat is that

 

 17   there are those who didn't enter that and were on

 

 18   it so there is always that question of what does it

 

 19   mean when you do it.  But, you are right, if you

 

 20   kept seeing that pattern, then it would be

 

 21   something you might wish to pursue further and ask

 

 22   for some additional studies.

 

                                                                32

 

  1             DR. CHESNEY:  Dr. Gorman?

 

  2             DR. GORMAN:  This is mainly for

 

  3   clarification from my reading of the labeling.  On

 

  4   page 7 of the label for this product there is a bar

 

  5   on the side and I wanted to know whether this was

 

  6   edited out of the label or is the present labeling

 

  7   wording which says that the safety and

 

  8   effectiveness of fexofenodine in pediatric patients

 

  9   under 6 years of age has not been established.  Is

 

 10   that in the label now or out of the label?

 

 11             DR. D. MURPHY:  It is not labeled under 6.

 

 12   Is that right?

 

 13             DR. GORMAN:  It is a question of the bar

 

 14   because it comes up several times later on in

 

 15   labeling.

 

 16             DR. D. MURPHY:  Right, right.  We will

 

 17   verify this but I think the point was that because

 

 18   there was no formulation that was available, it is

 

 19   not labeled under 6.

 

 20             DR. GORMAN:  I think one of the issues

 

 21   that was raised at the last meeting, and I would

 

 22   like to have it reemphasized again is that there is

 

                                                                33

 

  1   now data.  When we started this process two decades

 

  2   ago, that statement meant that there were no

 

  3   studies.  Now it means there may well be studies

 

  4   but it is not included in the label.  I noticed in

 

  5   the executive summary, which will be available on

 

  6   the web-based FDA data, that there is information

 

  7   about its use in children less than 6 months of

 

  8   age.

 

  9             DR. D. MURPHY:  I think you referred to

 

 10   the clinical pharmacology and biopharm study.

 

 11   Unfortunately, it doesn't have a page number but it

 

 12   is after the label.  It does say in there that no

 

 13   labeling changes for pediatric indication or dosing

 

 14   for children less than 6 years old will be made at

 

 15   this time because there are no age-appropriate

 

 16   formulations for fexofenodine for these children,

 

 17   and your point being that it was studied.  And,

 

 18   that is not going to be put in the label and I

 

 19   think that is an issue.

 

 20             DR. GORMAN:  That is the issue I wanted to

 

 21   raise and it will now be raised by others for the

 

 22   rest of the meeting.

 

                                                                34

 

  1             DR. CUMMINS:  Can I just provide one point

 

  2   of clarification?  The labels that we provide to

 

  3   you are ones that are publicly available and are

 

  4   the most recent labels.  Often the strikeouts are

 

  5   still present.  We download them from the labels

 

  6   that are posted on the web often--you know, that we

 

  7   post on the FDA website.  If you see a strikeout,

 

  8   as you see on page 7, then that strikeout will be

 

  9   removed in the published label by the company.

 

 10             DR. GORMAN:  Thank you.

 

 11             DR. CUMMINS:  You are welcome.

 

 12             DR. FILIE:  Given there are no further

 

 13   comments or questions, let me introduce the next

 

 14   speaker, Dr. Susan McCune.  Dr. McCune is a

 

 15   neonatologist whose previous experience includes

 

 16   academic neonatal practice at Johns Hopkins and

 

 17   Children's National Medical Center.  She recently

 

 18   received her masters degree in education and has

 

 19   worked on computer-based education models for

 

 20   pediatrics.  She will discuss two oncology

 

 21   products, topotecan and temozolomide.  Dr. McCune.

 

 22                    Topotecan and Temozolomide

 

                                                                35

 

  1             DR. MCCUNE:  Thank you very much, Dr.

 

  2   Filie.  Ladies and gentlemen of the committee and

 

  3   guests, Drs. Murphy told me to try to keep things a

 

  4   little bit light to keep you all awake and my Irish

 

  5   ancestry would allow me to tell shaggy dog stories

 

  6   but, unfortunately, I don't do very good jokes so I

 

  7   think we will just move along.

 

  8             As Dr. Filie mentioned, I will talk about

 

  9   two oncologic agents this morning.  The first is

 

 10   topotecan.  Topotecan, trade name Hycamtin, is an

 

 11   anti-tumor oncologic agent produced by

 

 12   GlaxoSmithKline.  The indication in adults is

 

 13   metastatic carcinoma of the ovary after failure of

 

 14   initial or subsequent chemotherapy and small cell

 

 15   cancer sensitive disease after failure of

 

 16   first-line chemotherapy.  There are no approved

 

 17   pediatric indications.  The original market

 

 18   approval was May 28, 1996 and the pediatric

 

 19   exclusivity was granted on November 20, 2002.

 

 20             I am going to tell you about the studies

 

 21   for exclusivity for this drug.  As you all

 

 22   mentioned, in terms of data that is available for

 

                                                                36

 

  1   the label, these studies were done based on what

 

  2   Dr. Iyasu told you already.  BPCA mandates that

 

  3   this information be available on the website and

 

  4   this information is available on the website,

 

  5   however, there were no changes to this label based

 

  6   on this information.

 

  7             The studies that were submitted for

 

  8   exclusivity were summaries of studies that were

 

  9   previously performed by the Pediatric Oncology

 

 10   Group.  They were initiated in 1992 and 1993.  This

 

 11   was a Phase 2 study in pediatric solid tumor that

 

 12   enrolled 108 patients that were less than 16 years

 

 13   of age.  The tumor types were Ewing's sarcoma,

 

 14   peripheral neuroectodermal tumor, neuroblastoma,

 

 15   osteoblastoma and rhabdomyosarcoma.  The study

 

 16   endpoint was tumor response rate.  Eighty-six

 

 17   percent of patients died, with 10 percent dying

 

 18   within 30 days of the last dose of topotecan.  The

 

 19   overall response rate was 8 percent but the

 

 20   response rate for patients with neuroblastoma was

 

 21   18 percent.  Of note, it is important to know that

 

 22   for alternative regimens using combinations of

 

                                                                37

 

  1   available drugs in pediatric patients with relapse

 

  2   neuroblastoma the response rates were 35-50

 

  3   percent.  In this case, no patients less than 2

 

  4   years of age showed any response.

 

  5             Eight of the 11 patients that died within

 

  6   30 days of the last dose of topotecan had

 

  7   progressive disease and 3 died with infection which

 

  8   is a known complication.  Forty-four percent of

 

  9   patients were hospitalized with adverse events,

 

 10   primarily febrile neutropenia, fever or sepsis.

 

 11             The Phase 2 study did determine a

 

 12   different dose from adults, a daily infusion for 5

 

 13   consecutive days every 21 days.  The adult dose is

 

 14   1.5 mg/m                                            2/day and the

pediatric dose that was given

 

 15   was either 1.4 mg/m                                                      

       2/day without granulocyte-colony

 

 16   stimulating factor or 2 mg/m                                             

                               2/day with

 

 17   granulocyte-colony stimulating factor.

 

 18             In terms of drug use trends in topotecan

 

 19   in the inpatient setting, between July, 2001 and

 

 20   June, 2003 there were 10.6 percent of discharges.

 

 21   Just to give you a rough idea, compared to the last

 

 22   drug which had a number of prescriptions, this was

 

                                                                38

 

  1   only 425 of 4,001.  Pediatric topotecan did

 

  2   increase annually in that time period, from 6.8 to

 

  3   18.6 percent.  It accounted for 407 discharges from

 

  4   29 CHCA free-standing pediatric hospitals, with the

 

  5   most frequent diagnosis being chemotherapy

 

  6   encounter followed by malignant neoplasm of the

 

  7   adrenal gland.  A significant limitation, as we

 

  8   have already discussed, of the analysis is that the

 

  9   FDA does not currently access data capture in the

 

 10   outpatient hospital clinic setting where most

 

 11   chemotherapy is administered.

 

 12             Now I am going to tell you about the

 

 13   adverse event reports for topotecan for the

 

 14   one-year post-exclusivity period.  There were 29

 

 15   total reports for all ages, 18 in the United

 

 16   States.  There were no pediatric reports that were

 

 17   submitted during this time.  Of note, in the 7-year

 

 18   period from 1996 there were some unlabeled

 

 19   pediatric reports, none of them during that 1-year

 

 20   post-exclusivity period.  There were 4 reports of

 

 21   convulsion, hypotension, edema  and speech

 

 22   disorder, and 3 reports each of arachnoiditis,

 

                                                                39

 

  1   ascites, Budd Chiari syndrome, caecitis and

 

  2   confusional state.

 

  3             In summary, the FDA will continue its

 

  4   routine monitoring of the adverse events in all

 

  5   populations.  I will stop here and take any

 

  6   questions on this particular drug.

 

  7             DR. CHESNEY:  Dr. Santana?

 

  8             DR. SANTANA:  I think I have made this

 

  9   point before and I will try to reinitiate it again.

 

 10   In contrast to some of the other drugs that we have

 

 11   in front of us, the oncology drugs are usually used

 

 12   in the setting of clinical research.  They are not

 

 13   used in the setting of common practice.  So, there

 

 14   is a wealth of data from protocols either initiated

 

 15   by the historically previous oncology groups or the

 

 16   current Children's Oncology Group and certainly by

 

 17   other large institutions like St. Jude's that do

 

 18   research in these drugs.  How is that data captured

 

 19   and reflected in these reports?  Because there is a

 

 20   wealth of adverse event data that is generated

 

 21   through that clinical research that will not show

 

 22   up through these voluntary reporting mechanisms but

 

                                                                40

 

  1   will show up in the databases of the clinical

 

  2   research infrastructure.

 

  3             DR. MCCUNE:  A lot of the reports that we

 

  4   get for these particular drugs are actually from

 

  5   study reports.  In terms of the studies that were

 

  6   done for exclusivity for this drug, they actually

 

  7   were, as you mentioned, part of the research

 

  8   protocols so they were independent studies

 

  9   conducted by the company.

 

 10             DR. SANTANA:  But I guess the point is

 

 11   that that is true but there is a lot more usage of

 

 12   this drug now, as you indicated in your brief

 

 13   summary of the trends of usage of this drug in

 

 14   pediatric oncology.  How is that data eventually

 

 15   going to make it into the adverse event reporting?

 

 16   Because it is not really part of the exclusivity

 

 17   because those studies have not been submitted for

 

 18   exclusivity.  Am I correct?

 

 19             DR. MCCUNE:  That is correct.

 

 20             DR. SANTANA:  These are studies that are

 

 21   ongoing.

 

 22             DR. MCCUNE:  That is correct.  This is the

 

                                                                41

 

  1   one-year post-exclusivity period.

 

  2             DR. SANTANA:  How will that data show up

 

  3   in the current study?

 

  4             DR. S. MURPHY:  It would have to come

 

  5   through the AERS.  It would have to be submitted to

 

  6   AERS for us to have that information.  Dr.

 

  7   Maldonado may want to comment, but the companies

 

  8   have to report any adverse events to the FDA.  So,

 

  9   the companies, you know, keep very close tabs on

 

 10   the medications, especially the medications that

 

 11   are in trials that are using their drugs.  So,

 

 12   there is a sort of cross-reference thing.  Then, it

 

 13   is even global with the pharmaceutical companies

 

 14   and with the international organizations with the

 

 15   FDA.  So, I think it is a very good question.  I

 

 16   think Don Mattison might want to make a comment,

 

 17   from NIH.

 

 18             DR. MATTISON:  Just a brief comment.  We

 

 19   are currently working with NCI and COG to develop

 

 20   full access to their databases and that information

 

 21   will be shared with FDA.

 

 22             DR. D. MURPHY:  Dr. Santana, I think if

 

                                                                42

 

  1   you look at what is in the label now, it just says

 

  2   that the effectiveness in children has not been

 

  3   demonstrated.  Then it goes ahead and it does

 

  4   describe the studies.  As you know, for cancer this

 

  5   has been a real issue because of the reasons you

 

  6   have stated.  The label is marketing approval and

 

  7   if it is not approved for that indication, you

 

  8   know, the agency is in this quandary of how do you

 

  9   make information available when you don't want to

 

 10   give a de facto indication that doesn't exist?  So,

 

 11   that is the tension here.  Depending on the

 

 12   product, depending on what comes out of the

 

 13   exclusivity studies if we don't have sufficient

 

 14   evidence to say it is efficacy and, as you know,

 

 15   and I don't want to say this over and over again,

 

 16   but these studies are not powered to do that.  So,

 

 17   how do we make that information available has been

 

 18   difficult.

 

 19             I think what they have done here is that

 

 20   they have been able to put into--by saying it has

 

 21   not been demonstrated, first, and saying yet we

 

 22   looked and here is what we found in a very limited

 

                                                                43

 

  1   way, and then having some adverse event reporting

 

  2   that came out.  Now, does it happen for every

 

  3   product, every time?  Not always because it may be

 

  4   that there were other issues with the studies and

 

  5   then what you may end up with in the label if there

 

  6   is a particular safety thing, they would say it was

 

  7   studied in so many kids; it wasn't effective or we

 

  8   couldn't determine effectiveness but we are going

 

  9   to tell you about these adverse events.  So, that

 

 10   can happen.  The adverse events in those studies

 

 11   could be put into the label if it is a safety

 

 12   issue.

 

 13             DR. SANTANA:  I guess what I am getting at

 

 14   is that the information that is derived from

 

 15   granting exclusivity is for the studies that the

 

 16   sponsor has put forth to reach that point.

 

 17             DR. D. MURPHY:  Right; that is correct.

 

 18             DR. SANTANA:  But there is another wealth

 

 19   of data that is being generated.  As I understand

 

 20   it, unless it is throught the sponsor or through

 

 21   some other mechanism that data becomes available to

 

 22   the FDA it is not part of the information that we

 

                                                                44

 

  1   have in front of us today or in the future.

 

  2             DR. D. MURPHY:  Well, it is required to be

 

  3   reported to the FDA.  It is required to be reported

 

  4   and if the agency sees a signal, then there is a

 

  5   re-review of the data and a determination if that

 

  6   additional information needs to be entered into the

 

  7   label.  I would say that if a researcher had access

 

  8   to data that they were concerned about and saw that

 

  9   it wasn't in the label, it is perfectly appropriate

 

 10   to ask--you know, again, it is a requirement.

 

 11   Companies get into big trouble if they have adverse

 

 12   events that they don't report to us.

 

 13             The other issue--I am not saying it

 

 14   happens, but if somehow you thought something

 

 15   wasn't getting reported, it is perfectly

 

 16   appropriate to call the agency and say I am aware

 

 17   of this; make sure you got those reports.

 

 18             DR. SANTANA:  I want to make it clear for

 

 19   the public record that I am not raising issues with

 

 20   this drug or the next oncology drug.  I am trying

 

 21   to understand the process.  I just want to make

 

 22   that clear.

 

                                                                45

 

  1             DR. D. MURPHY:  Yes, and we want to make

 

  2   it clear that it is part of companies' standard

 

  3   reporting activity.  Sam, maybe you could say

 

  4   something about the routine things that go on in

 

  5   reporting both during a trial and after a product

 

  6   is marketed.

 

  7             DR. MALDONADO:  Both of you are completely

 

  8   right.  Companies are not going to get in trouble

 

  9   by not reporting.  That is very enforceable.  A lot

 

 10   of not reported events happen when physicians don't

 

 11   report to companies.  So, that is where the problem

 

 12   is; it is the education.  We are not only talking

 

 13   about sending in the reports, but sending them

 

 14   within 15 days of occurrence.  Most of the

 

 15   non-reporting happens because of lack of education

 

 16   from clinicians.  In clinical trials it happens

 

 17   much less, or probably very, very close to zero

 

 18   because there is monitoring by the company.  Actual

 

 19   people go there and make sure they are doing it.

 

 20   Outside clinical trials it is more difficult

 

 21   because you cannot police physicians so it is up to

 

 22   them to report. But once it is reported to the

 

                                                                46

 

  1   companies, it is reported to the FDA and the FDA,

 

  2   of course, can always come to a company and check

 

  3   if we are doing it and actually FDA does that.

 

  4             DR. D. MURPHY:  I think what Sam has said

 

  5   is really important.  If a physician sees an

 

  6   adverse event on a product, particularly if you put

 

  7   them on a product, take them off and put them back

 

  8   on--you know, if you have evidence, but even if you

 

  9   don't, if you put a child on a product and you have

 

 10   some serious event and you are not sure whether it

 

 11   is related or not, you don't have to make

 

 12   attribution.  This is one of the problems I think

 

 13   physicians don't understand.  You don't have to

 

 14   determine individually that this product caused

 

 15   this adverse event.  If physicians would, please,

 

 16   make it part of their public health rule to report

 

 17   adverse events that they think are serious to the

 

 18   agency and to the company, I mean, that is a double

 

 19   way--or either way, you know, whichever way you

 

 20   know how to get that information in.  It will get

 

 21   to us if it gets to the company or it can come to

 

 22   us directly.  So, I would like to keep adding that

 

                                                                47

 

  1   commercial.  It is a very important part of

 

  2   activity.  I have been out there; I have practiced

 

  3   medicine and I know I haven't done it when I should

 

  4   have.  So, it is just a plea that we keep putting

 

  5   that out there because you can see how important it

 

  6   can become.

 

  7             DR. CHESNEY:  Dr. O'Fallon?

 

  8             DR. O'FALLON:  There is one other issue

 

  9   that is a possible problem.  I don't know these

 

 10   particular studies that COG is doing but if they,

 

 11   indeed, have closed patient accrual before the

 

 12   exclusivity period it is entirely possible that the

 

 13   acute toxicities wouldn't be available at this

 

 14   time.  You know, not all the data in these clinical

 

 15   trials gets reported out until the final study is

 

 16   done.  I mean, the company had to know about it

 

 17   ahead of time, but during this exclusivity period

 

 18   there maybe weren't any from those trials.

 

 19             DR. D. MURPHY:  I think that brings up the

 

 20   other issue just of any follow-up post-trial.  As

 

 21   you know, there was a legislative mandate also to

 

 22   put the 1-800 MedWatch number on labels and that

 

                                                                48

 

  1   process is proceeding.  I don't have any idea when

 

  2   actually you will see it but it is continuing to

 

  3   move forward.

 

  4             DR. CHESNEY:  Dr. Ebert?

 

  5             DR. EBERT:  Just a follow-up to that, is

 

  6   it feasible or even reasonable with these drugs

 

  7   that are specifically under exclusivity for the FDA

 

  8   to make pediatricians more aware of the fact that

 

  9   they are under this particular scrutiny?  And,

 

 10   would it heighten their level of interest with

 

 11   regards to reporting adverse events?

 

 12             DR. D. MURPHY:  Joan has a suggestion for

 

 13   you later today I think about maybe one way of

 

 14   doing it.  We have been trying to do that in a

 

 15   number of ways by working with the American Academy

 

 16   of Pediatrics newsletter that goes out and doing

 

 17   annual updates of changes in the label, talking

 

 18   about exclusivity, but I think you bring up a good

 

 19   point--have we really made an issue in that

 

 20   reporting about changes in label about reporting

 

 21   adverse events?  No.  And, that is a good point and

 

 22   we will take that back and pursue that as an

 

                                                                49

 

  1   additional piece of information we should try to

 

  2   get out to pediatricians, family practice, people

 

  3   who are taking care of children.  We are working

 

  4   with the Academy on the CME activity so that we can

 

  5   put in some case studies that might bring that up.

 

  6             DR. S. MURPHY:  Joan, just one more point,

 

  7   there are really two ways of reporting adverse

 

  8   events.  One is to the FDA and the other is to the

 

  9   companies.  The larger pharmaceutical companies

 

 10   have these 1-800 numbers and if you call and you

 

 11   say you have an adverse event, you are immediately

 

 12   put in touch with the Pharm.D. who has a whole

 

 13   scheme of questions to ask you right away.  All

 

 14   those reports, like Sam said, do go back to the FDA

 

 15   and the seriousness of the report triggers certain

 

 16   times to report it.  Having been on the other side

 

 17   in a pharmaceutical company, I was in charge of a

 

 18   drug that had a lot of adverse reactions and we

 

 19   were constantly reviewing all the cases that came

 

 20   in.  The company will often send somebody out to

 

 21   the hospital to look at the records and make sure

 

 22   of the accuracy of the reporting.  So, it is taken

 

                                                                50

 

  1   incredibly seriously on both sides.

 

  2             DR. CHESNEY:  Thank you.  We can move on

 

  3   to the next speaker.

 

  4             DR. MCCUNE:  Actually, I am doing the next

 

  5   drug.  You get to listen to me again.  The next

 

  6   drug I am going to talk about is temozolomide.  The

 

  7   trade name for this is Temodar.  Once again, this

 

  8   is an oncologic agent produced by Schering Plough

 

  9   Research Institute.  The indication in adults is

 

 10   that the capsules are indicated for the treatment

 

 11   of adult patients with refractory anaplastic

 

 12   astrocytoma, in other words, patients at first

 

 13   relapse who have experienced disease progression on

 

 14   a drug regimen containing a nitrosourea and

 

 15   procarbazine.  In pediatrics there are no approved

 

 16   pediatric indications.  The original market

 

 17   approval was August 11, 1999; the pediatric

 

 18   exclusivity was granted November 20, 2002.

 

 19             Once again, I am going to tell you about

 

 20   the studies for exclusivity.  These are available

 

 21   on the website.  In addition, for this particular

 

 22   label safety information is included in the

 

                                                                51

 

  1   pediatric section of the precautions part of the

 

  2   label and it does include a description of the

 

  3   clinical studies that were completed.

 

  4             The studies that were submitted for

 

  5   exclusivity were one Phase 1 and two Phase 2

 

  6   open-label, multicenter studies.  The Phase 1 study

 

  7   was dose escalation in 27 patients with advanced

 

  8   non-CNS and CNS cancers.  The first Phase 2 study

 

  9   was in 63 patients with recurrent brain stem glioma

 

 10   and high grade astrocytoma.  The second Phase 2

 

 11   study, a cooperative group-sponsored study, was in

 

 12   122 patients with various recurrent CNS tumors.

 

 13   The patients ranged in age from 1 to 23 years of

 

 14   age, with the majority of patients between 3 and 17

 

 15   years of age.

 

 16             The primary endpoint for these studies was

 

 17   tumor response rate.  In the first Phase 2 study

 

 18   there was 1 complete response and 3 partial

 

 19   responses among 27 patients.  In the second study

 

 20   there were no complete responses or partial

 

 21   responses in the brain stem glioma patients and no

 

 22   complete response and 12 percent partial responses

 

                                                                52

 

  1   in the high grade astrocytoma patients.  In the

 

  2   third study the overall response rate, combined

 

  3   complete response and partial response rate, was 5

 

  4   percent.  Only 1 patient achieved complete response

 

  5   and 5 patients had partial responses.

 

  6             Safety was assessed in 204 patients at

 

  7   doses of 100-200 mg/m                                                     

            2/day daily for 5 days every

 

  8   28 days.  The toxicity profile that was seen was

 

  9   similar to adults.  The most common adverse events

 

 10   that were reported were dizziness, neuropathy,

 

 11   paresthesia, nausea/vomiting, constipation and

 

 12   myelosuppression.

 

 13             Just to give you an idea of the drug use

 

 14   trends in the outpatient setting for temozolomide,

 

 15   the number of prescriptions dispensed has nearly

 

 16   doubled over the past 3 years from 50,000 in 2001

 

 17   to 93,000 in 2003, with the top prescribers, as you

 

 18   can imagine, being oncology/neoplastic, neurology

 

 19   and hematology.  Of note, only 1 percent of

 

 20   temozolomide prescriptions were written by

 

 21   pediatricians.

 

 22             The pediatric population of 1-16 years of

 

                                                                53

 

  1   age accounted for a small number of temozolomide

 

  2   prescriptions, 3.1 percent in 2002 and 3.9 percent

 

  3   in 2003, with the most frequent diagnosis being

 

  4   malignant neoplasm of the brain both in adults and

 

  5   pediatric patients.

 

  6             In terms of outpatient sales, they have

 

  7   been on the rise, from 1.8 million capsules to 2.2

 

  8   million capsules in the last 2 years, with the

 

  9   majority of sales through retail channels, 80

 

 10   percent of them going to chain and independent

 

 11   pharmacies and other retail channels.

 

 12             CHCA data demonstrated from 2002 to June,

 

 13   2003 that there were only 17 pediatric discharges

 

 14   associated with this drug.

 

 15             The limitations to drug use data in the

 

 16   outpatient setting for these drugs are important to

 

 17   note because we don't have sources that

 

 18   specifically examine outpatient hospital clinics

 

 19   where chemotherapy treatments are provided.  What

 

 20   is important to note though is that the retail

 

 21   sales do capture a number of those sources and it

 

 22   is felt that most of the use of this drug is

 

                                                                54

 

  1   captured through assessment of outpatient use.

 

  2             In terms of adverse event reporting for

 

  3   the post-exclusivity period from November, 2002 to

 

  4   December, 2003 there were 250 reports in all ages,

 

  5   160 of them in the United States.  There were 5

 

  6   unduplicated pediatric reports, 2 of them in the

 

  7   United States, all with serious outcomes and 1

 

  8   death.  There were 4 females and 1 male.  Three of

 

  9   the patients were aged 2-5 years; 2 of the patients

 

 10   6-11 years.  There was one patient each for the

 

 11   diagnoses of blastoma, adrenal metastatic

 

 12   neuroblastoma, anaplastic astrocytoma,

 

 13   medulloblastoma and brain stem tumor.

 

 14             The clinically significant unlabeled

 

 15   adverse events could be divided into 5 groups.  One

 

 16   was brain edema; 1 was death.  Another, hemangioma

 

 17   acquired; another ITP and another myelodysplastic

 

 18   syndrome.  All of these, although not specifically

 

 19   delineated in the label, are potentially related to

 

 20   either a labeled process or the underlying disease

 

 21   state.

 

 22             Just to take each one of these

 

                                                                55

 

  1   individually, brain edema in the patient was

 

  2   associated with concomitant radiation therapy.  The

 

  3   death was potentially due to the underlying

 

  4   condition.  The acquired hemangioma was potentially

 

  5   related to either the underlying condition, the

 

  6   concomitant medication or the radiation therapy.

 

  7   The ITP was a potentially labeled event or

 

  8   secondary to the underlying condition.  The

 

  9   myelodysplastic syndrome was also a potentially

 

 10   labeled event or secondary to the underlying

 

 11   condition.

 

 12             Just to give you a brief synopsis of these

 

 13   5 cases, the first was a 3 year-old that was

 

 14   treated for pineal blastoma who died of an

 

 15   unspecified cause.

 

 16             The second was a 6 year-old who was

 

 17   treated for recurrent anaplastic astrocytoma, was

 

 18   on concomitant medications including radiation

 

 19   therapy, and following temozolomide use, a

 

 20   cavernous hemangioma was noted on MRI.  Of note, it

 

 21   was not previously seen on prior MRIs.  Following

 

 22   temozolomide treatment, this patient also had

 

                                                                56

 

  1   thrombocytopenia requiring transfusions and was

 

  2   diagnosed with ITP and myelodysplastic syndrome.

 

  3   This patient was discharged with an improved

 

  4   clinical status 18 days after admission.

 

  5             The third case is a 4 year-old treated for

 

  6   medulloblastoma who suffered an infection and there

 

  7   was no outcome of the event that was documented.

 

  8             The fourth case is a 4 year-old treated

 

  9   for metastatic neuroblastoma who developed

 

 10   thrombocytopenia, anemia and fever which were

 

 11   managed with transfusions and antibiotics.  She

 

 12   recovered without sequelae and was given a second

 

 13   cycle of temozolomide without recurrence.

 

 14             The final case is an 8 year-old who was

 

 15   treated for brain stem tumor.  Routine MRI revealed

 

 16   radiation-induced cerebellum edema requiring

 

 17   hospitalization for intracranial drainage.  This

 

 18   patient was subsequently discharged in stable

 

 19   condition.

 

 20             In summary, for temozolomide there have

 

 21   been described both labeled and unlabeled adverse

 

 22   events.  The unlabeled events have also been

 

                                                                57

 

  1   reported in adults and are not unique to

 

  2   pediatrics, and the FDA will continue to do routine

 

  3   monitoring of adverse events in all of the

 

  4   populations.

 

  5             DR. CHESNEY:  Thank you very much.  I just

 

  6   wanted to bring to the committee's attention the

 

  7   fact that at 9:30, although we are getting

 

  8   significantly behind with the very full agenda, the

 

  9   FDA has asked us to address question one, which is

 

 10   at the back of the packet that we were given today

 

 11   with the agenda on it, which involves process

 

 12   issues.  So, I think unless you have specific

 

 13   questions related to this drug, if they are process

 

 14   issues, we will have an hour to discuss that later

 

 15   on.  So, does anybody have specific comments

 

 16   regarding this drug?  Shirley?

 

 17             DR. S. MURPHY:  Dr. Chesney, Dr. Starke

 

 18   from the Pulmonary Division has some late-breaking

 

 19   information on the first drug that we discussed.

 

 20   He was just going to tell us a follow-up on a

 

 21   question that the committee had, what the bar was

 

 22   beside the label.

 

                                                                58

 

  1             DR. STARKE:  I am Dr. Starke, from

 

  2   Pulmonary and Allergy Division.  I am a medical

 

  3   team leader.  I went upstairs and double-checked

 

  4   the label for you since there was a cross-out

 

  5   there.  That was simply something that was caught

 

  6   as the final label was approved.  The current

 

  7   labeling does say for 6 months and older.

 

  8             I just want to make the comment that even

 

  9   though the studies were done down to 6 months of

 

 10   age and, as you know, certain other antihistamines

 

 11   may be approved down to 2 for SAR and 6 months for

 

 12   PAR, this drug was not approved below age 6 because

 

 13   there was no marketed formulation.  A

 

 14   non-marketable formulation was used which, of

 

 15   course, is an issue which you may want to address.

 

 16   Thank you.

 

 17             DR. CHESNEY:  Thank you.  If there are no

 

 18   additional questions on your presentation, which I

 

 19   thank you for, I think we can move on to the next

 

 20   speaker.

 

 21             DR. MCCUNE:  It is my privilege to

 

 22   introduce Dr. Harry Gunkel to you.  He is the only

 

                                                                59

 

  1   person standing between me and the privilege of

 

  2   saying that I am the most junior member of the

 

  3   Pediatric Drug Development Office.  Like me, he is

 

  4   a neonatologist who has extensive experience in

 

  5   private practice, the pharmaceutical industry and

 

  6   academic medicine.  Many of you may know him for

 

  7   his significant work on surfactant.  He is going to

 

  8   talk to you today about two ophthalmologic

 

  9   anti-infective agents.

 

 10                  Moxifloxacin and Ciprofloxacin

 

 11             DR. GUNKEL:  Thank you, Susie.  Hello.  As

 

 12   Susie said, the next two products on the list are

 

 13   both ophthalmic antibacterials, both

 

 14   fluoroquinolones.  The first is ciprofloxacin,

 

 15   known under the trade name Ciloxan and sponsored by

 

 16   Alcon Laboratories.  It is indicated in adults and

 

 17   children greater than 1 year of age in a solution

 

 18   dosage form, and adults and children greater than 2

 

 19   years of age in the ointment dosage form for the

 

 20   treatment of bacterial conjunctivitis caused by the

 

 21   organisms shown on the slide.  The solution form is

 

 22   also indicated for corneal ulcer.  The original

 

                                                                60

 

  1   market approval was in 1990 and pediatric

 

  2   exclusivity was granted in January, 03.

 

  3             Drug use data shows that dispensed

 

  4   prescriptions for Ciloxan decreased slightly over

 

  5   the period of exclusivity.  Almost half of the

 

  6   prescriptions for this drug were for children

 

  7   between 1 and 16 years of age, and pediatricians

 

  8   wrote about a third of the prescriptions during the

 

  9   exclusivity period.

 

 10             The most common indication for the

 

 11   prescription was conjunctivitis, other or

 

 12   unspecified, and Ciloxan was the most mentioned

 

 13   product for this indication in pediatric patients.

 

 14             During the exclusivity period there were 9

 

 15   total reports for all ages; 3 were from the U.S.

 

 16   The age was not specified for 2 of the 9 reports.

 

 17   There were no pediatric reports.  We will continue

 

 18   to monitor the adverse event reports, of course.

 

 19             The next drug is moxifloxacin, also

 

 20   sponsored by Alcon Laboratories, also an ophthalmic

 

 21   antibacterial drug.  It is indicated for adults and

 

 22   children 1 year of age or greater for the treatment

 

                                                                61

 

  1   of bacterial conjunctivitis caused by a number of

 

  2   susceptible organisms, aerobic gram negative and

 

  3   gram positive organisms.  The market approval for

 

  4   this product was April of '03, less than a year

 

  5   ago.  So, that will become pertinent when we look

 

  6   at the data in just a moment.  Exclusivity was

 

  7   granted before market approval, in January of '03.

 

  8             Since approval didn't occur until April of

 

  9   last year, the drug use and adverse event data

 

 10   cover less than a 1-year period, unlike the other

 

 11   products you are reviewing today.  About 800,000

 

 12   prescriptions were dispensed since approval in