1

DEPARTMENT OF HEALTH AND HUMAN SERVICES

FOOD AND DRUG ADMINISTRATION

CENTER FOR DRUG EVALUATION AND RESEARCH

 

 

 

 

 

 

DERMATOLOGIC AND OPHTHALMIC DRUGS

ADVISORY COMMITTEE

 

 

 

 

 

 

 

 

 

 

Thursday, May 23, 2002

8:30 a.m.

 

 

 

 

 

 

Kennedy Ballroom

Holiday Inn

8777 Georgia Avenue

Silver Spring, Maryland

2

PARTICIPANTS

Lynn A. Drake, Acting Chair

Karen M. Templeton-Somers, Executive Secretary

MEMBERS

Elizabeth A. Abel, M.D.

Roselyn E. Epps, M.D.

Robert Katz, M.D.

Lloyd E. King, Jr., M.D., Ph.D.

Paula Knudson (Consumer Representative)

Sharon S. Raimer, M.D.

Ming T. Tan, Ph.D.

CONSULTANTS (VOTING)

Warwick L. Morison, M.B., B.S., M.D.,

M.R.C.P.

Seth R. Stevens, M.D.

J. Richard Taylor, M.D.

GUEST (NON-VOTING)

Robert Swerlick, M.D.

CBER, FDA

Ezio Bonvini, M.D.

Louis Marzella, Ph.D.

Jay Seigel, M.D.

Karen Weiss, M.D.

3

C O N T E N T S

Call to Order and Opening Remarks:

Lynn A. Drake, Acting Chair 4

Introductions 5

Conflict of Interest Statement:

Karen M. Templeton-Somers, Ph.D. 7

BLA 125036, alefacept, Biogen, Inc.

Introduction:

Ezio Bonvini, M.D. 19

Sponsor Presentation, Biogen, Inc.

Overview:

Burt Adelman, M.D. 14

Clinical Experience:

Akshay K. Vaishnaw., M.D., Ph.D. 28

Clinical Safety:

Goria Vigliani, M.D. 59

Alefacept Risk Benefit Profile:

Mark Lebwohl, M.D. 77

FDA Presentation

Louis Marzella, M.D., Ph.D. 90

Questions from the Committee 126

Open Public Hearing

Gail M. Zimmerman 202

Diane Lewis 205

Maryellen Crawford 210

Sean Morton 212

Alan Menter, M.D. 215

Committee Discussion and Vote 222

4

1 P R O C E E D I N G S

2 Call to Order and Opening Remarks

3 DR. DRAKE: Hello. My name is Lynn Drake.

4 I am from Harvard Medical School, the Massachusetts

5 General Hospital. I am pleased to be the chair of

6 this meeting.

7 The first thing I would like to do is open

8 the meeting. This is the Dermatologic and

9 Ophthalmologic Drugs Advisory Committee. First of

10 all, I would like to welcome all the members of the

11 committee. As you know, you had fairly extensive

12 briefing documents. You have had to take a lot of

13 your personal time to review all this and take your

14 time to come here today. We are so appreciative

15 that you have given that volunteer time to help

16 review the product before us today.

17 I would like to thank the FDA staff, the

18 whole team. The briefing documents were actually

19 very well done. They were concise. They were easy

20 to read and it was clear that effort had been put

21 into it. So I do want to thank the whole FDA staff

22 and team for giving us such a nice group of

23 documents to work from. The preparation was

24 obvious.

25 I would also like to thank the sponsor for

5

1 bringing forward a new drug. You know, we have

2 patients with bad disease and we are always

3 appreciative that you take the time to try to

4 develop a new drug that will help our patients. So

5 we are very grateful to you for bringing forth this

6 new drug.

7 I also would like to welcome all the

8 guests who are here today. I think public interest

9 in the proceedings in important and significant and

10 so we are grateful. I am particularly pleased that

11 we have some documented participants in the open

12 public hearing. That is delightful to see because

13 we don't always have that and that kind of input

14 just makes us do our job better.

15 So, having said all that, the first person

16 I would like to introduce is Dr. Karen Templeton-Somers, my

17 Executive Officer for this. She has

18 done a yeoman's amount of work. You can't imagine.

19 Karen, I would like to thank you very much in

20 advance for all the work you have done and all the

21 help you are going to give me today. She keeps me

22 out of trouble. In case you guys don't know what

23 she does, her primary job is to keep me out of

24 trouble from here on out.

25 The first thing I would like to do so that

6

1 everybody knows who everybody is, I would like to

2 go around the table, have the committee members

3 introduce themselves sand your affiliation. I

4 would like to start with Dr. Swerlick.

5 One of the rules--we have these ridiculous

6 rules here. We have to speak into the mike.

7 Introduction of Committee

8 DR. SWERLICK: Robert Swerlick. I am an

9 Associate Professor of Dermatology at Emory

10 University.

11 DR. TAYLOR: Richard Taylor. I am

12 Professor at the University of Miami and Chief of

13 Dermatology at the Miami V.A. Hospital.

14 DR. ABEL: Elizabeth Abel. I am Clinical

15 Professor of Dermatology at Stanford in California

16 and in private practice in Mountain View.

17 MS. KNUDSON: I am Paula Knudson. I am

18 the IRB Coordinator for the University of Texas

19 Health Science Center in Houston.

20 DR. STEVENS: I am Seth Stevens. I am

21 from University Hospitals of Cleveland. I am Chief

22 of Dermatology at the Cleveland V.A. and at Case

23 Western Reserve University.

24 DR. KATZ: I am Robert Katz, in the

25 private practice of dermatology in Rockville,

7

1 Maryland, Clinical Associate Professor of

2 Dermatology at Georgetown University Hospital.

3 DR. TEMPLETON-SOMERS: Karen Somers,

4 Executive Secretary to the committee, FDA.

5 DR. MORISON: Lloyd Morison, Professor of

6 Dermatology at Johns Hopkins University.

7 DR. EPPS: Dr. Roselyn Epps, Chief of the

8 Division of Dermatology, Children's National

9 Medical Center which is affiliated with George

10 Washington University.

11 DR. KING: Lloyd King, Chief of

12 Dermatology at Vanderbilt University and at the

13 National V.A.

14 DR. TAN: Ming Tan, Associate Member of

15 Biostatistics, St. Jude Children's Research

16 Hospital.

17 DR. RAIMER: I'm Sharon Raimer, Chairman

18 of Dermatology at the University of Texas in

19 Galveston.

20 DR. BONVINI: I am Ezio Bonvini, Division

21 of Monoclonal Antibodies, Center for Biologics.

22 DR. MARZELLA: I am Louis Marzella,

23 Division of Clinical Trials in the Center for

24 Biologics.

25 DR. WEISS: Karen Weiss, Division of

8

1 Clinical Trials, Center for Biologics.

2 DR. DRAKE: Terrific. Next, I would like

3 to ask Dr. Somers to please inform us about our

4 conflict of interest statement.

5 Conflict of Interest Statement

6 DR. TEMPLETON-SOMERS: The following

7 announcement addresses conflict of interest with

8 regard to this meeting and is made a part of the

9 record to preclude even the appearance of such at

10 the meeting.

11 Based on the submitted agenda for the

12 meeting and all financial interests reported by the

13 committee participants, it has been determined that

14 all interests in firms regulated by the Center for

15 Drug Evaluation and Research present no potential

16 for an appearance of a conflict of interest at this

17 meeting with the following exceptions.

18 Dr. Ming Tan has been granted waivers

19 under 18 U.S.C. 208(b)(3) and 595(n)(4) of the FDA

20 Modernization Act for his ownership of stock in a

21 competitor. The stock is valued at between $5,001

22 to $25,000. Dr. J. Richard Taylor has been granted

23 waivers under 28 U.S.C. 208(b)(1) and 505(n)(4) of

24 the FDA Modernization Act for his employer's

25 contract with a competing firm. The value of the

9

1 contract is less than $100,000 per year.

2 These waivers permit Dr. Tan and Dr.

3 Taylor to participate in the committee's

4 deliberations and vote considering Biologic License

5 Application Submission Tracking Number 125036,

6 Amevive, alefacept, sponsored by Biogen,

7 Incorporated.

8 A copy of these waive statement may be

9 obtained by submitting a written request to the

10 agency's Freedom of Information Office, Room 12A30

11 of the Parklawn Building.

12 With respect to FDA's invited guest, Dr.

13 Robert Swerlick has a reported interest that we

14 believe should be made public to allow the

15 participants to objectively evaluate his comments.

16 Dr. Swerlick has a financial interest in Immunex

17 and Enbrel.

18 In the event that the discussions involve

19 any other products or firms not already on the

20 agenda for which an FDA participant has a financial

21 interest, the participants are aware of the need to

22 exclude themselves from such involvement and

23 exclusion will be noted for the record.

24 With respect to all other participants, we

25 ask in the interest of fairness that they address

10

1 any current or previous financial involvement with

2 any firm whose products they may wish to comment

3 upon.

4 Thank you

5 DR. DRAKE: Thank you, Dr. Somers.

6 We have a very packed agenda today. There

7 is a lot of information to be imparted. I will ask

8 the presenters to please stick to your allotted

9 time. If you go over, I will probably have to try

10 to signal you in some capacity because I want to

11 make sure we have plenty of time at the end for the

12 really important stuff.

13 I would also remind the committee that

14 brevity is wonderful and I will try to remember

15 that same rule, myself. So if we can keep

16 everything as concise as possible, we will move

17 through the agenda and accomplish everything.

18 With that, let's start. I think the first

19 presenter is Dr. Bonvini from the Division of

20 Monoclonal Antibodies, Office of Therapeutics

21 Research and Review.

22 Dr. Bonvini, welcome.

23 BLA 125036, alefacept, Biogen, Incidence.

24 Introduction

25 DR. BONVINI: Good morning.

11

1 [Slide.]

2 Madame Chairman, distinguished members of

3 the advisory committee, ladies and gentlemen, good

4 morning.

5 On behalf of the Center for Biologics, I

6 would like to thank you for your participation in

7 today's discussion of alefacept for the treatment

8 of chronic plaque psoriasis.

9 [Slide.]

10 My duty today in the next few minutes is

11 to introduce you to the BLA review committee and

12 introduce the molecular entity under discussion and

13 provide a brief immunological background for the

14 discussion of the clinical data for alefacept. I

15 am Ezio Bonvini and I serve as the Chairman and the

16 product review for alefacept.

17 The clinical review was the responsibility

18 of Lou Marzella and Electra Papadopoulos.

19 Pharmacologic and toxicology review were performed

20 by Laureen Black and David Green. The statistical

21 review was performed by Chao Wang. Bioresearch

22 monitoring supervision was under the responsibility

23 of Jose Tavarezpagan. Establishing and

24 manufacturing review for alefacept was alefacept

25 was the responsibility of Chiang Syin and Carol

12

1 Rehkopt. I would like to acknowledge the excellent

2 regulatory management of Beverly Connor and Lori

3 Tull.

4 [Slide.]

5 The molecule for today's discussion is

6 alefacept, also known as Amevive and also

7 identified in a number of publications as LFA3Tip.

8 Alefacept is a fusion protein comprising the human

9 LFA molecule fused with the human IgG-1 FC portion.

10 This molecule dimerizes through the disulfate bond

11 mediated via the IgG portion of the molecule.

12 As a background to introduce the

13 immunosuppressive mechanism of alefacept, I will

14 briefly review how T-cell activation occurs.

15 [Slide.]

16 The activation of T-lymphocyte is a

17 complex mechanism that is centered on the

18 recognition by the clonotypic T-cell receptor of

19 antigen. Now, that doesn't occur in soluble form

20 and the recognition by the T-cell receptor occurs

21 in the context of the major histocompatibility

22 complex of antigen-presenting cells. In addition

23 to the clonal T-PIC receptor, the interaction is

24 assisted by an invariant component, the CD8 or CD4

25 which interacts with the MHC Class 1 or 2

13

1 respectively.

2 The interaction with the T-cell receptor

3 and the antigen is a low affinity. For a stable

4 association to occur, other molecules intervene and

5 these are called accessory molecules. A critical

6 accessory molecule for the interaction of T-cell

7 with antigen presenter cells is C28 on the surface

8 of T-cells which interact with B7.1 and B7.2.

9 [Slide.]

10 But, additional molecules are also

11 involved in mediating this interaction and they

12 include a number additional molecules among which

13 LFA3 is one which interacts with CD2 on the surface

14 of T-cells.

15 Now the combination of signal via the T-cell

16 receptor and the costimulatory molecules lead

17 to a productive response resulting in lymphokine

18 secretion such as IL2, interferon, and a number of

19 chemotactic lymphokines such as IL8 which lead the

20 T-cell expansion and may be involved in the

21 proinflammatory process underlying the disease

22 under consideration with kerotinocyte proliferation

23 and differentiation.

24 [Slide.]

25 Alefacept can interfere with this

14

1 mechanism in the context of this complex

2 interaction by either scavenging the physiologic

3 interaction of LFA3 with CD2, by itself engaging CD2

4 Now, in addition to this competitive

5 mechanism which occur at affinities relatively low

6 and similar to those involving the interaction of

7 endogenous LFA3 with CD2, another mechanism is

8 involved and that is the redirection of a second

9 class of cells, the macrophages and NK cells, via

10 engagement of the Fc receptor through the Fc

11 component of the alefacept fusion protein. This

12 delivers a signal which induces activation of NK

13 cells which delivers a lethal hit.

14

15 The susceptibility to NK-mediated lysis of

16 the cells may be different

17 depending on the subtype of cells under

18 consideration.

19 While the exact mechanism of the

20 susceptibility of T-cells to alefacept-mediated

21 lysis is not fully understood, the T-cell depletion

22 induced by alefacept and its potential for

23 competition with endogenous LFA3-CD2 interaction

24 are central to our discussion of the clinical

25 activity of alefacept and will be touched upon by

15

1 Dr. Marzella and Biogen in their review.

2 [Slide.]

3 CD2 is expressed prevalently on T-lymphocytes and

4 there is expression on NK cells. B-lymphocytes are largely

5 negative for CD2 expression

6 with only some precursors in the bone marrow being

7 positive.

8 [Slide.]

9 The concludes my brief introduction on the

10 immunological background. I need to remind this

11 committee that we are still addressing some

12 outstanding issues pertaining to the manufacturing

13 of alefacept that remain to be resolved. The

14 agency and Biogen are working close together and

15 are trying to address this issue in a timely

16 fashion.

17 I think I stuck to my time. This

18 concludes my presentation. I could take questions

19 or just give the podium to Biogen.

20 DR. DRAKE: I think you did a great job.

21 Do any of the committee members have a pertinent

22 question about the presentation? I'm sure we will

23 have some later. Thank you, sir.

24 DR. BONVINI: Okay.

25 DR. DRAKE: I think we have a latecomer to

16

1 the meeting, but we are delighted. Dr. Seigel, I

2 presume?

3 DR. SEIGEL: Yes.

4 DR. DRAKE: Welcome. We are delighted to

5 have you here.

6 DR. SEIGEL: Thank you. Pleased to be

7 here.

8 DR. DRAKE: I had just complimented you

9 and your team for a very nice presentation of the

10 documents. We are very grateful when it is so well

11 done.

12 DR. SEIGEL: Thank you very much.

13 DR. DRAKE: Moving forward, now it is time

14 for the sponsor which is Biogen for their

15 presentations. I believe the overview will be

16 given by Dr. Adelman.

17 Sponsor Presentation, Biogen, Inc.

18 Introduction

19 DR. ADELMAN: Thank you, Madame

20 Chairwoman. Good morning, members of the panel,

21 colleagues from CBER and members of the audience.

22 [Slide.]

23 My name is Burt Adelman. I am the

24 Executive Vice President of Research and

25 Development at Biogen. Much of our research

17

1 efforts at Biogen are focused on understanding

2 autoimmunity and developing therapeutic strategies

3 to treat autoimmune diseases. Today, as a result

4 of these efforts, we are pleased to be here to

5 discuss alefacept, a new agent that we have

6 developed for the treatment of chronic plaque

7 psoriasis.

8 [Slide.]

9 Our presentation will focus on data that

10 we believe supports the following indication.

11 Alefacept is indicated for the treatment of

12 patients with chronic plaque psoriasis who are

13 candidates for systemic or phototherapy. Alefacept

14 is a parenteral agent and we recommend a dosing

15 regimen as listed here, once per week dosing for 12

16 weeks.

17 The drug can be administered either as a

18 7.5 milligram intravenous bolus injection once a

19 week or a 15 milligram intramuscular injection once

20 a week. Repeat courses can be given after a 12-week rest

21 period.

22 [Slide.]

23 Our agenda this morning is listed here. I

24 will provide a brief overview of the product. Dr.

25 Akshay Vaishnaw, Medical Director at Biogen, will

18

1 talk about the clinical efficacy of the alefacept

2 and describe the pharmacodynamics. Dr. Gloria

3 Vigliani, Vice President of Medical Research at

4 Biogen will speak about the clinical safety

5 profile. Finally, we have invited Dr. Mark

6 Lebwohl, a distinguished expert in the field of

7 psoriasis to provide a perspective from the

8 clinical view on the risk-benefit profile of

9 alefacept.

10 [Slide.]

11 In addition to Dr. Lebwohl, we are

12 fortunate to have with us a number of other

13 distinguished consultants. These include Dr.

14 Richard Cooper, a hematologist, Professor of

15 Medicine at the Medical College of Wisconsin; Dr.

16 David Margolis, Associate Professor of Dermatology

17 and Epidemiology at the University of Pennsylvania

18 and Dr. James Krueger, Associate Professor and

19 physician at the Rockefeller University. Dr.

20 Krueger heads the Laboratory of Investigative

21 Dermatology at that Institution.

22 Although they will not be making formal

23 presentations, they are here to help with the

24 discussion and answer any questions that may arise.

25 [Slide.]

19

1 Now, to begin my review. Chronic plaque

2 psoriasis is recognized to be a T-cell mediated

3 disease. Men and women are affected equally.

4 Although it is recognized that there is a strong

5 genetic component to this disorder, the exact genes

6 that drive the disorder have yet to be identified.

7 In appearance, the skin lesion of

8 psoriasis is a circumscribed red raised plaque.

9 These plaques are often itchy and scaly and can

10 crack and bleed. Psoriasis can also be associated

11 with a number of systemic manifestations, the most

12 common of which is psoriatic arthritis.

13 Individuals with moderate to severe psoriasis

14 typically have lesions covering 10 percent or more

15 of their body-surface area. As you will have seen

16 in the briefing document that we distributed, a

17 number of the patients in our studies actually had

18 skin involvement of up to 98 percent of their body-surface

19 area. Psoriasis is a life-long disease

20 and, as yet, there is no cure.

21 [Slide.]

22 Here is a picture of the disease that we

23 are speaking about. This is a patient from one of

24 our Phase 3 studies, a gentleman with moderate to

25 severe chronic plaque psoriasis. It is not hard to

20

1 understand that this disease, in addition to the

2 clinical manifestations, has a debilitating impact

3 on a patient's life.

4 John Updike, in his essay, At War with My

5 Skin, describes poignantly his own personal

6 experience with psoriasis. "They glance at me and

7 glance away pained. My hands and my face mark me.

8 The name of the disease, spiritually speaking, is

9 Humiliation."

10 [Slide.]

11 This statement powerfully captures the

12 psychosocial burden that many individuals with

13 psoriasis suffer. In fact, this has been studied

14 and, to some degree, quantified. Quality of life

15 is identified as being severely impacted in

16 patients with moderate to severe psoriasis. The

17 impact is similar to that of other serious diseases

18 such as chronic congestive heart failure and

19 advanced diabetes mellitus.

20 Understandably, these effects correlate

21 with the increased risk of substance abuse,

22 depression and suicidal ideation commonly seen in

23 the psoriasis population. Common comorbidities of

24 psoriasis include obesity, heart disease, diabetes

25 and hepatitis.

21

1 For all these reasons, patients and their

2 physicians are often searching for new therapies

3 and patients with advanced psoriasis often seek out

4 and are commonly treated with aggressive therapies.

5 [Slide.]

6 Current therapies to treat chronic plaque

7 psoriasis are listed here, systemic therapies.

8 There are two types. In the upper part of the

9 slide, I have indicated the disease-suppressive

10 therapies. In the lower part are the remittive

11 therapies.

12 The suppressive therapies, methotrexate,

13 retinoids and cyclosporine effectively treat the

14 disease as long as the patient takes them. When

15 therapies are withdrawn, there is usually

16 reasonably rapid return of disease, hence the label

17 suppressive. Remittive therapies such as PUVA an

18 UVB, light-based therapies, can provide disease-free

19 periods. However, to obtain these results,

20 patients must undergo frequent and repeat treatment

21 cycles.

22 Each of these important therapies is

23 associated with one or more toxicity that is

24 significant, commonly observed and often limits it

25 use.

22

1 [Slide.]

2 For example, methotrexate can cause

3 hepatic fibrosis and patients who receive over a

4 gram and a half of methotrexate often are required

5 to have a liver biopsy to determine whether they

6 can receive additional therapy. Cyclosporine is

7 commonly associated with nephrosis and, therefore,

8 patients cannot take cyclosporine continuously for

9 more than a year.

10 Phototherapy with PUVA has been documented

11 to increase patient risk for squamous-cell

12 carcinoma and melanoma. So, again, significant

13 limitations for therapy.

14 So, while these therapies provide

15 meaningful efficacy, their use also imposes

16 significant risk. In an effort to balance toxicity

17 and maintain reasonable disease control,

18 dermatologists have evolved a strategy of disease

19 management based on rotating the available

20 therapies. Clearly, new therapies, particularly

21 remittive agents that can induce a long duration of

22 effect will favorably impact this strategy of

23 rotational therapy.

24 It is to address this significant unmet

25 need that we have developed alefacept.

23

1 [Slide.]

2 To understand the rationale behind the

3 development of alefacept as a new immunomodulator,

4 I would like to briefly review the pathobiology of

5 psoriasis. As indicated a few slides ago,

6 psoriasis is clearly recognized to be a T-cell-mediated

7 disorder. In particular, memory T-cell

8 subsets play a critical role in a pathogenesis of

9 the psoriatic plaque.

10 In this section from a skin biopsy of a

11 patient with psoriasis, memory T-cells are seen

12 infiltrating the skin underlying the proliferative

13 response. These active cells are derived from CD4

14 and CD8 cells and are identified by a

15 characteristic cell-surface marker called CD45RO-positive.

16 It can be stained for and these cells

17 can, therefore, be uniquely identified.

18 Once in the skin, again as we see here,

19 these activated CD45RO-positive cells release a

20 spectrum of inflammatory mediators that stimulate

21 kerotinocyte proliferation and blood-vessel growth

22 resulting in the characteristic psoriatic plaque.

23 [Slide.]

24 The cells that I have described can be

25 identified in the blood and in the lymph organs.

24

1 This cartoon indicates the composition of

2 leukocytes in the blood. You can see that memory

3 CD45RO-positive cells are constituent of the T-cell

4 CD4 and CD8 population within the blood and they

5 can be distinguished from naive cells by this

6 characteristic marker.

7 Our data suggest that alefacept

8 selectively targets CD4 and CD8 memory cells and it

9 does this through its activity against the CD2

10 ligand on memory cells.

11 [Slide.]

12 Dr. Bonvini has taken you through this and

13 with somewhat more elegant slides. Perhaps he will

14 lend them to me in the future. But I will take you

15 through this mechanism again.

16 A naive T-cell that has never previously

17 seen antigen will interact with antigen-presenting

18 cells by way of the MHC and T-cell receptor. But,

19 as already mentioned, this interaction is

20 inadequate to result in T-cell activation and,

21 importantly, costimulatory pathways mediated

22 through coupling of LFA-3 and CD2 and B7 and CD28

23 are also necessary. In fact, this cartoon is,

24 itself, a simplification and there are other

25 additionally important costimulatory pathways.

25

1 As a result of these events, the naive T-cell

2 becomes activated. During the activation

3 process, a number of characteristic changes occur.

4 The cells proliferate so, in fact, there would be

5 more cells here than just the one and a number of

6 changes occur on the surface. In particular, there

7 is increased expression of CD2 on the surface of

8 these CD45RO-positive cells.

9 This conversion from the CD2 low state to

10 the CD2 high state is what we think imparts the

11 selectivity of alefacept to the CD45RO-positive

12 memory cell.

13 Just, also, by way of historical

14 background, LFA3 was actually cloned at Biogen and,

15 very early on, we understood the significance of

16 the LFA3-CD2 interaction and that is why we have

17 chosen this particular pathway to develop a drug

18 that interferes with this process.

19 [Slide.]

20 Here, again, is a picture of alefacept.

21 As you can see, it includes the extracellular

22 domain of human LFA3 fused to a portion of human

23 IgG1 and is, therefore, called a fusion protein.

24 It is expressed as a dimer which is held together

25 by cysteine bonds and, although it looks like an

26

1 immunoglobulin, it is not an immunoglobulin. It is

2 a fusion protein.

3 Now, the sequence is entirely human and

4 that is why there is very little antigenicity

5 associated with the use of this.

6 [Slide.]

7 I would like to review again alefacept

8 actions as are illustrated in this slide.

9 Alefacept can block LFA3 CD2 interactions thereby

10 inhibiting reactivation of memory T-cells. As

11 indicated here, alefacept would bind to CD2 and

12 stearically interfere with the docking to an

13 antigen-presenting cell.

14 Again, as Dr. Bonvini already indicated,

15 another effect is also mediated by alefacept.

16 Alefacept combined via the FC receptor on certain

17 cells such as natural killer cells and induce a

18 pro-apoptotic response. This is mediated through

19 the release of a protein called granzyme which

20 initiates apoptosis in the memory T-cell resulting

21 in its loss.

22 This is a generalized model. We believe

23 that this model applies at the doses that are

24 recommended for use to treat psoriasis but there

25 may be specifics about how this mechanism works in

27

1 the skin, in the blood and in lymph tissue and we

2 are fortunate to have Dr. Krueger here with us

3 today who has studied this extensively and,

4 perhaps, during the question period, he can comment

5 further on the specifics of this effect.

6 [Slide.]

7 This mechanism of action was tested in a

8 blinded placebo-controlled dose-ranging Phase-II

9 study in approximately 230 patients with moderate

10 to severe psoriasis. I have illustrated the

11 results here, in particular looking at the effects

12 on CD4-positive memory cells. So these would be

13 CD45RO-positive cells that are also CD4 positive

14 and CD4 positive naive T-cell, unactivated T-cells,

15 that would not express CD45RO.

16 What you can see--this was a dose-response

17 study. Here is the twelve-week dosing period and

18 this is a twelve-week follow-up period. This is

19 the placebo dose and here are increasing doses of

20 alefacept. You can see that, with increasing

21 doses, there is increased reduction in the number

22 of CD4-positive memory T-cells and the cell counts

23 start to recover after discontinuation.

24 In contrast, there is minimal effect, if

25 any, on the naive T-cells during the same dosing

28

1 period. It was these pharmacodynamic effects

2 coupled with the clinical effects that we observed

3 in this study that led to the development of the

4 clinical program for alefacept in chronic plaque

5 psoriasis. We are here to discuss those results

6 today.

7 [Slide.]

8 I would like to provide some additional

9 background on the overall program. We have

10 conducted an extensive toxicology program to

11 support alefacept development. In fact, we have

12 completed 35 toxicology studies in nonhuman

13 primates. We are fortunate because a nonhuman

14 primate responds somewhat similarly to humans in

15 that we can observe impacts on T-cell numbers and

16 we can look at the effect that this may have in the

17 lymph nodes and we can watch recovery.

18 For testing purposes, we have used

19 regimens up to 20 milligrams per kilogram IV weekly

20 for one year. This dosing regimen, obviously,

21 greatly exaggerates the recommended dosing regimen

22 in people, both in terms of magnitude of drug

23 delivered and length of continuous exposure.

24 [Slide.]

25 Here I have summarized the results of the

29

1 toxicology program for you. Alefacept was well-tolerated in

2 these animals. We observed reversible

3 decreases in lymphocyte counts, both in blood and

4 lymphoid tissues. No opportunistic infections were

5 observed in any treated animal and no reproductive

6 toxicity was observed.

7 I would like to comment on one observation

8 that was outlined for you in the briefing document.

9 In a single cyno monkey receiving 20 milligrams per

10 kilogram of alefacept weekly, we diagnosed the

11 occurrence of a B-cell lymphoma. This monkey was

12 part of a long-term treatment study and, as I have

13 mentioned, received a very high dose continuously

14 for 28 weeks.

15 In fact, this dose is the equivalent of

16 622 clinical courses. So we made this observation

17 in the setting of a highly exaggerated dosing

18 schedule. This was the only observation of

19 lymphoma in over 200 animals treated across various

20 preclinical studies.

21 [Slide.]

22 This next slide briefly outlines the

23 clinical program for alefacept which you will be

24 hearing in much more detail later this morning. We

25 have conducted 18 clinical studies and treated

30

1 1,357 patients with chronic plaque psoriasis and

2 240 healthy volunteers.

3 The core of our presentation focuses on

4 three randomized double-blind placebo-controlled

5 studies in patients with chronic plaque psoriasis.

6 One is a Phase 2 study and the other two Phase 3

7 studies. These studies will be discussed in detail

8 by Dr. Vaishnaw.

9 We, at Biogen, are committed to

10 understanding both the short and long-term safety

11 issues associated with the introduction of

12 alefacept as we would be with any new drug being

13 introduced into the community. We believe that

14 active monitoring of patients on therapy for

15 extended periods of time, even after a product is

16 approved, should be a key component of an

17 integrated, long-term safety and development

18 program.

19 For these reasons, most of the patients

20 coming out of our randomized clinical trials have

21 been given the opportunity to enter into a

22 comprehensive extended safety dosing study. In

23 fact, at this point in time, over 800 patients are

24 currently in extended safety dosing studies.

25 Already, some of these individuals have received as

31

1 many as five treatment courses over a three-year

2 period of time and it is our intention to extend

3 this program indefinitely and probably to expand

4 it.

5 [Slide.]

6 Because alefacept targets memory T-cells,

7 we have already begun to study its effects in other

8 autoimmune disorders with a T-cell-mediated

9 etiology. Currently, in addition to psoriasis, we

10 are studying psoriatic arthritis, rheumatoid

11 arthritis and sclera derma and, in fact, we

12 summarized for you, in your briefing document, the

13 results of a small study in psoriatic arthritis.

14 [Slide.]

15 Throughout the development history of this

16 program, we have had a close collaboration with our

17 colleagues at CBER. We are grateful to them for

18 their interest and guidance in all aspects of the

19 preclinical, clinical and manufacturing programs.

20 The regulatory history of alefacept is

21 outlined here. In August of 1996, we had a pre-IND

22 meeting with the agency and, shortly thereafter,

23 launched our program in the United States. In

24 1999, and end-of-Phase-II meeting was held to

25 discuss our positive findings. After agreement

32

1 with the agency on the design of the Phase 3

2 program, we moved forward to begin the studies that

3 we will be discussing today.

4 Now, importantly, the safety database in

5 this document is consistent with ICH guidelines.

6 In July of last year, we met again with CBER to

7 discuss our Phase 3 results and plan for filing an

8 electronic biologics license application. In

9 August of 2001, we filed the application which we

10 are happy to be here to discuss with you today.

11 Now, in March of 2002, we provided the agency with

12 an extensive safety update to this document.

13 Now it is my pleasure to introduce Dr.

14 Vaishnaw who will take you through clinical details

15 of our program. Thank you for your attention.

16 Clinical Experience

17 DR. VAISHNAW: Thank you.

18 [Slide.]

19 Madame Chairperson, members of the panel,

20 ladies and gentlemen, good morning. I am Akshay

21 Vaishnaw. I am a member of the medical team at

22 Biogen. I have been involved with the development

23 of alefacept.

24 I shall be describing two components of

25 the clinical experience to you today, namely the

33

1 efficacy and pharmacodynamic aspects of the

2 program.

3 [Slide.]

4 I have divided the efficacy part of the

5 presentation beginning with a brief overview of the

6 Phase 2 study and following with a detailed

7 analysis of the Phase 3 studies both the IM and IM

8 protocols. I will then move to a description of

9 the quality-of-life improvement seen after

10 alefacept therapy and close with a discussion of

11 the efficacy in some important subpopulations of

12 patients.

13 [Slide.]

14 There are three randomized placebo-controlled

15 trials that are at the core of the

16 program; a Phase 2 IV study and two Phase 3

17 studies, one by the IM route and one by the IV

18 route.

19 You can see that in the Phase 2 study, we

20 dosed patients on a body-weight basis. Here you

21 can see that is indicated as dosing in milligram

22 per kilogram. Other studies during Phase 2

23 indicated that body weight did not significantly

24 influence the pharmacokinetics of alefacept and,

25 therefore, in Phase 3, we transitioned to the more

34

1 convenient fixed-dose regimens as indicated here.

2 As you look to the right of this slide,

3 you can see that a substantial number of patients,

4 in fact over 1300 patients, were enrolled in these

5 three studies making them some of the largest

6 chronic-plaque-psoriasis studies ever.

7 [Slide.]

8 The findings from the Phase 2 study were

9 published by Drs. Charles Ellis and Gerry Krueger

10 in an article in The New England Journal of

11 Medicine last year and their major findings were

12 summarized as follows. They detected that

13 alefacept was associated with clinically meaningful

14 efficacy and it was superior to placebo. They

15 determined that it had a significant duration of

16 benefit.

17 Patients that had cleared their disease

18 had a median time to retreatment of ten months.

19 With respect to T-cells, given the mechanism of

20 action, they clearly illustrated that alefacept was

21 selective for reductions in memory T-cells with

22 sparing of naive T-cells. Importantly, these

23 changes correlated with efficacy outcomes. This

24 validated the therapeutic rationale in the approach

25 to Phase 3. Finally, the Ellis and Krueger study

35

1 allowed us to pick the optimum dose group for Phase

2 3.

3 With that, I want to turn to the Phase 3

4 studies.

5 [Slide.]

6 At baseline in the Phase 3 studies, all

7 the important background demographic and disease-severity

8 factors were well balanced. I want to

9 consider some factors related to disease status at

10 baseline.

11 Here you see data for the two Phase 3

12 studies, the IM and IV protocols. The median

13 duration of disease at baseline ranged between

14 eighteen and nineteen years. In other words, these

15 patients had established chronic plaque psoriasis.

16 If you look at the next three rows, the

17 body-surface area involvement, the PASI score and

18 the physician global, each reveals that patients

19 had moderate to severe chronic plaque psoriasis at

20 baseline.

21 [Slide.]

22 Let me illustrate that by considering the

23 BSA score. The median BSA at baseline ranged

24 between 21 and 22 percent in these studies. Now,

25 if we imagined that one palm size is about 1

36

1 percent of our body-surface area, then 22 percent

2 average involvement is extensive chronic plaque

3 psoriasis and a significant burden of disease to

4 these patients at baseline.

5 That conclusion is supported by the median

6 PASI score in the mid-15s and the physician global

7 assessment where over 80 percent of patients had

8 disease severity ranging between moderate to

9 severe.

10 [Slide.]

11 I have already mentioned the PASI. PASI

12 will be central to a lot of our discussions

13 regarding efficacy today. PASI is, in fact, an

14 acronym of the Psoriasis Area and Severity Index.

15 It is a widely used tool in psoriasis clinical

16 trials in order to quantify and follow disease

17 activity over time. It is a composite measure and

18 involves measurement of erythema, induration,

19 desquamation and the extent of body-surface area

20 involved.

21 Those four parameters are evaluated over

22 four parts of the anatomy; the head, the trunk, the

23 upper limbs and the lower limbs. Those data are

24 put into a formula resulting in a composite score

25 which ranges from 0 to 72. 0 is clear or healthy

37

1 skin. 72 is disease of maximum severity.

2 A score between the range of 10 and 30

3 typically summarizes patients with moderate to

4 severe chronic plaque psoriasis.

5 [Slide.]

6 Three endpoints will be discussed with

7 respect to the clinical trials we are reviewing

8 today. These are PASI 75--that is a 75 percent or

9 greater reduction from baseline disease severity

10 with respect to the PASI tool, a very stringent

11 endpoint. The next endpoint is PASI 50, a

12 50 percent or greater reduction from baseline

13 disease severity. Finally, the third stringent

14 endpoint is the physician global assessment of

15 almost clear or clear.

16 These two endpoints were read out both two

17 weeks after the last dose in the studies and also

18 in what we term the overall response rate. I want

19 to illustrate what I mean by that on the following

20 diagram.

21 [Slide.]

22 Here is a typical randomized placebo study

23 comparing placebo to alefacept. On the left-hand

24 part of the diagram, you can see the dosing

25 interval. Patients are receiving injections for

38

1 the first twelve weeks. On the right-hand side,

2 you can see they are followed for another twelve

3 weeks. That 12-plus-12 interval we term a course

4 of alefacept therapy.

5 Now, the primary efficacy endpoint was

6 conducted as a landmark analysis two weeks after

7 last dose at this single time point. Given that in

8 Phase 2 and in other studies we had determined that

9 alefacept patients often reach maximal efficacy at

10 other times often late in the follow-up interval

11 here, we also determined the overall response rate

12 for patients that achieved PASI 75 and the other

13 endpoints at any time during the course of therapy.

14 [Slide.]

15 Before we actually consider the efficacy

16 data, I want to, with the use of a few pictures,

17 consider what a PASI 50 and PASI 75 response is

18 like. It can be difficult to conceptualize them in

19 the abstract.

20 Here is a patient on the left who, at

21 baseline, has had extensive chronic plaque

22 psoriasis effect from the midline, the area above

23 the buttocks and the backs of the arms. This is a

24 patient with a score of 18.7 by the PASI 2 and

25 baseline. After treatment, the score is 5.7. This

39

1 patient has an almost 70 percent reduction in PASI.

2 This patient would not qualify for the

3 primary-efficacy endpoint of PASI 75 but would

4 qualify for PASI 50. She doesn't qualify for PASI

5 50. She doesn't qualify for PASI 75 because she

6 has never attained 75 or greater.

7 [Slide.]

8 Contrasting that to the PASI 75 response,

9 on the left you see a young person with extensive

10 disease again affecting the torso and the lower

11 limbs. His score is 34.3 at baseline. After

12 treatment, his score is 4.2. The percentage

13 positive reduction is 88. This gentleman would

14 qualify as a PASI 75 responder.

15 [Slide.]

16 With that background, I want to review the

17 two major studies, first the Phase 3 IM study.

18 [Slide.]

19 In the Phase 3 IM study, patients were

20 screened and randomized to one of three arms,

21 placebo or alefacept 10 milligrams or alefacept 15

22 milligrams. They received the injections once a

23 week IM for 12 weeks on the left-hand side of the

24 diagram and then there was a 12-week follow-up

25 interval. The primary efficacy endpoint was read

40

1 out as a landmark analysis two weeks after last

2 dose. The primary endpoint was PASI 75.

3 Note that the endpoint was read out

4 without the use of disqualifying medications; by

5 this, I mean major, high-potency topical steroids

6 or the major systemic antipsoriatic agents, and the

7 range of UV therapies that are commonly used.

8 If patients used any of those

9 disqualifying medications prior to the primary

10 efficacy endpoint, they were classified as a

11 treatment failure. If patients did not show up for

12 the primary efficacy-endpoint visit, they were,

13 again, classified as a treatment failure. This is

14 a relatively conservative approach when documenting

15 efficacy data.

16 The rules regarding disqualifying

17 medications also apply to all the other efficacy

18 data we are going to review today.

19 [Slide.]

20 In the Phase 3 IM study, PASI 75 score two

21 weeks after last dose was 21 percent in the 15

22 milligram group and 5 percent in the placebo group.

23 This difference was highly statistically

24 significant and the Phase 3 IM study, therefore,

25 met the primary efficacy endpoint.

41

1 In the middle you can see that, in the 10-

2 milligram group, 12 percent of patients attained

3 the endpoint contributing to this nice dose

4 response between placebo and 15 milligrams.

5 The findings from this PASI 75 tool was

6 strongly supported by an independent measurement,

7 namely the physician global of almost clear or

8 clear.

9 [Slide.]

10 Here you can see on the right that 14

11 percent of patients in the 15-milligram group

12 cleared their disease versus 5 percent in the

13 placebo group. The difference was highly

14 statistically significant.

15 [Slide.]

16 Finally, the third of the endpoints also

17 supported the conclusion that alefacept was

18 superior to placebo with 42 percent of patients in

19 the 15-milligram group achieving the endpoint, 18

20 percent in placebo. So, over a series of

21 endpoints, all stringent, we have demonstrated that

22 alefacept monotherapy was significantly superior to

23 placebo.

24 [Slide.]

25 I have just conveyed some of the landmark

42

1 analyses two weeks after last dose. I want to

2 contrast the findings from those to those for the

3 overall response rate where patients were achieving

4 the endpoint at times other than just two weeks

5 after last dose.

6 On the right, you can see patients who hit

7 PASI 75 at any time during a course of therapy as

8 shown with 33 percent in the yellow in the 15-milligram

9 group achieving PASI 75. This is

10 significantly greater than the 21 percent by the

11 landmark analysis.

12 You see increments for all three treatment

13 groups on the right compared to the left, but the

14 data on the right conveyed that these patients in

15 the alefacept group had more sustained responses

16 than those in the placebo group here, and we

17 therefore believe that the overall response-rate

18 data for each of the endpoints we will be

19 discussing today reflect the true clinical

20 attributes of alefacept and what patients can

21 expect to experience in terms of the course of

22 therapy.

23 [Slide.]

24 I am going to turn now to the Phase 3 IV

25 study. Patients were screened here and randomized

43

1 to one of three arms, Cohort 1, Cohort 2 or Cohort

2 3. All three cohorts received two courses of

3 therapy, as indicated. Each course was 24 weeks

4 long.

5 Cohort 1 received alefacept in the first

6 course followed by alefacept in the second. Cohort

7 2 received alefacept followed by placebo. Cohort 3

8 received placebo followed by alefacept. The

9 primary efficacy endpoint, as for the IM study, was

10 PASI 75 two weeks after last dose, again without

11 the use of disqualifying medications.

12 The advantage of this type of study, apart

13 from the primary efficacy endpoint for the placebo-

14 controlled component of the program here was we

15 could also ask the question, did repeated courses

16 of alefacept result in evidence for incremental

17 efficacy by examining outcomes in Course 2 for

18 alefacept with the outcomes in Course 1.

19 By examining outcomes for Cohort 2 who

20 received a single course of treatment, when they

21 are off therapy for this 36-week period, we could

22 determine how sustained was the efficacy after 12

23 injections. So, with that, let me actually turn

24 now to the data.

25 [Slide.]

44

1 Here we have summarized the three

2 endpoints we have spoken of, the outcomes two weeks

3 after last dose in the first course. Let's focus

4 first on the far left, PASI 75, which is the

5 primary efficacy endpoint for this study. 14

6 percent of patients in the alefacept group achieved

7 the endpoint, 4 percent in the placebo group. This

8 difference was highly statistically significant.

9 So, again, for the Phase 3 IV study, we met the

10 primary efficacy endpoint as prespecified.

11 The data from the other two endpoints

12 again support the conclusions from the primary

13 efficacy endpoint, the physician global, alefacept

14 11 percent, placebo 4 and, for PASI 50, 38 percent

15 of patients achieved the endpoint versus 10 percent

16 in the placebo.

17 Now, examining outcomes for Cohort 1 in

18 the second course, we detected evidence of

19 incremental efficacy as shown here in yellow. You

20 see that, for each of the three endpoints I have

21 just described, the response rates increased in the

22 second course. Considering the PASI 75, the

23 response rate when from 14 to 23 percent, a very

24 significant increment, similarly, for physician

25 global and PASI 50.

45

1 [Slide.]

2 Now, to contrast those landmark analyses

3 two weeks after last dose in each course to the

4 overall response rate where patients responded at

5 other times during the course of therapy.

6 Concentrating first on PASI 75, far left,

7 you can see in the alefacept subgroup 28 percent of

8 patients responded at some point during the course

9 of the first course of therapy. This is a doubling

10 of the primary efficacy-endpoint data, 14 percent.

11 The difference here is statistically highly

12 significantly superior to placebo.

13 The evidence of an incremental rise in

14 these overall response rates is also seen for the

15 physician global and PASI 50 with over half the

16 patients achieving PASI 50 in the first course of

17 therapy.

18 If we look at the overall response rates

19 in the second course, we see evidence of

20 incremental efficacy, 37 percent of PASI 50, 30

21 percent for patients clearing their disease and 64

22 percent--that is, almost two-thirds of patients--achieved

23 PASI 50 during the second course of

24 therapy.

25 [Slide.]

46

1 Now, an important area of ummet need and

2 an important attribute of potentially new therapies

3 or agents that could put the disease into

4 remission; we were interested to calculate whether

5 alefacept had disease-remittive properties and, to

6 do that, we analyzed the data from Cohort 2 who

7 received the twelve weeks of treatment and 36 weeks

8 of follow up.

9 We calculated the duration of remission

10 for those patients that had achieved the most

11 stringent endpoint, PASI 75, during Course 1. The

12 duration of remission was defined as the time spent

13 in response at PASI 50 or better.

14 The median duration of remission, as

15 defined, was seven months. This appears to be

16 significant and to suggest that alefacept is a

17 disease-remittive type of agent and the first

18 systemic immunotherapy to have this type of

19 property. The data also consolidates the findings

20 from the Ellis and Krueger paper in The New England

21 Journal of Medicine where they also demonstrated

22 efficacy duration suggestive of disease-remittive

23 properties.

24 [Slide.]

25 Here is a graphical representation of this

47

1 same data. We are looking at the PASI-50-or-better

2 response in those that achieved PASI 75, Cohort 2

3 in the Phase 3 IV study. The Kaplan-Meier curve

4 tracks the duration of time patients are in a

5 response of PASI 50 or better.

6 You can see 50 percent of patients are at

7 this level of response for 211 days or more. So,

8 again PASI 50 or better is maintained for a period

9 of seven months for the median number of patients.

10 [Slide.]

11 The other important area of unmet need for

12 chronic-plaque-psoriasis patients is the tremendous

13 quality-of-life deficit these patients suffer. We

14 were obliged to understand whether alefacept

15 treatment improved the quality of life.

16 [Slide.]

17 To do this, we used the tool termed the

18 DLQI, or the Dermatology Life Quality Index first

19 described by Finlay and Kahn in 1994. It has been

20 used fairly widely in dermatologic studies

21 including psoriasis studies.

22 On the left, you see the data for the

23 changes in DLQI for placebo versus 7.5 milligrams

24 IV for the Phase 3 IV study. On the right, you are

25 seeing the corresponding data for the Phase 3 IM

48

1 study.

2 Looking on the left at the Phase 3 IV

3 data, there is a reduction in the DLQI score for

4 those in the placebo group, 11 to 9.9. I should

5 remind you that the reduction in score is an

6 improvement in quality of life. In the alefacept,

7 7.5 milligram group, there is a significant

8 reduction from 11 to 7.6.

9 The conclusion that alefacept is

10 associated with statistically significant

11 reductions in DLQI scores was also seen in the

12 Phase 3 IM study as indicated on the right here.

13 [Slide.]

14 These types of data don't fully convey the

15 potential quality-of-life improvements patients can

16 experience. To begin to do that, the next two

17 slides address the issue of to what extent are

18 patients really improving.

19 Firstly, to what extent did patients

20 improve if they achieved PASI 75, if they achieved

21 PASI 50 or they achieved physician global. These

22 data are from the responders in the Phase 3 IV

23 study. It is a pooled analysis irrespective of

24 whether the patient was in the placebo group or in

25 the alefacept groups. Looking at the PASI 75

49

1 response, you can see the score transition is from

2 11 pretreatment to 2.4 if you achieve PASI 75 with

3 alefacept. That is a significant reduction.

4 Similarly, if you go to the right, you can

5 look at the physician global. The transition is

6 from 10.4 to 2.4, again a very extensive reduction.

7 Those data are not surprising because these are

8 very stringent endpoints but we were surprised to

9 see that, for PASI 50, the score went from 11.6 to

10 4.2, another very significant improvement in the

11 quality of life.

12 This data begins to give insight into the

13 importance of PASI 50 as an important endpoint for

14 these patients to achieve with this burden of

15 disease.

16 [Slide.]

17 Finally, to give the ultimate granularity

18 of what quality-of-life improvement means to

19 patients, here are data from the actual

20 subcomponents of the DLQI score for 15 milligram

21 group in the Phase 3 IM study. There are similar

22 data for the other treatment groups. What I want

23 to discuss is the extent to which patients that

24 reported being at the severe end of the scale for

25 each of these questions changed from baseline to

50

1 two weeks after last dose.

2 So it is a five-point scale and at

3 baseline patients are meant to fill out a

4 questionnaire saying how much embarrassment did

5 they suffer. The most extreme end of the scale is

6 very much or a lot. The proportion who answered at

7 that level at baseline was 64 percent consistent

8 with the disease burden they have.

9 After twelve weeks of treatment, 27

10 percent of patients in the 15-milligram group

11 experienced the same level of embarrassment. Their

12 impact on daily activities transitioned from 21

13 percent having very great difficulties to 7 percent

14 and as you go on down the table.

15 This is across the treatment groups. If

16 you look at the same data for patients who

17 responded to the various endpoints, you see even

18 further improvements or greater improvements in

19 these important quality-of-life domains.

20 [Slide.]

21 Finally, I would like to close the issue

22 with a discussion of outcomes in some important

23 subpopulations.

24 [Slide.]

25 First, the outcomes as a function of

51

1 disease severity at baseline. There appear to be a

2 lot of ways to quantify disease severity. We have

3 chosen one standard approach here. Severe disease

4 is body-surface area greater than 30 percent at

5 baseline. Less severe disease is body-surface area

6 involved in less than 30.

7 On the right, you can see the proportions

8 of patients with a BSA greater than 30 who achieve

9 the primary efficacy endpoint, 13.8 in the

10 alefacept group in Phase 3 IV study versus 5.6 in

11 the placebo group. The difference is significant.

12 The same magnitude is seen in the BSA

13 less-than-30 group, 16.2 in the alefacept group

14 versus 4.1. We have concluded that alefacept

15 efficacy is not significantly influenced by

16 baseline disease severity and patients with a broad

17 range of disease severity can be helped by the

18 drug.

19 [Slide.]

20 Now, a similar pooled analysis of all

21 Phase 3 patients so that we have very big numbers

22 here was done for patients based upon their prior

23 response status. About 80 percent of patients in

24 the Phase 3 studies reported having one of the

25 major systemic antipsoriatic agents or UV therapy

52

1 prior to entering into our studies.

2 Those patients were classified based upon

3 their responses as having no change or worsening on

4 the previous therapies, improving on previous

5 therapy or no prior treatment; i.e., naive to the

6 previous therapies.

7 Then, for each of those groups, we

8 assessed the primary efficacy endpoint. For those

9 that had not changed on the previous treatments or

10 worsened, 20.2 percent responded to alefacept. 3.1

11 responded in the placebo group. This difference

12 was highly statistically significant. The same

13 kind of data is seen for those that also improved

14 on previous treatments and for those that were

15 naive to previous treatments.

16 So this analysis supports the conclusion

17 that alefacept is efficacious in a broad range of

18 patients irrespective of their response to previous

19 agents.

20 [Slide.]

21 To summarize the efficacy part of the

22 presentation, we have concluded that alefacept is

23 effective in reducing psoriasis disease activity.

24 We have done this by three independent randomized

25 placebo-controlled studies. These encompass both

53

1 the IV and the IM routes. The data, as we have

2 discussed, are consistent and robust across all

3 endpoints and in important subpopulations of

4 patients.

5 In the Phase 3 IV study, we demonstrated a

6 greater evidence of response with the second course

7 of therapy--in other words, incremental efficacy--and we

8 demonstrated extended durations of remission

9 of seven months in patients that achieved PASI 75

10 during the Phase 3 IV study.

11 Finally, and most importantly, perhaps,

12 alefacept therapy has been shown to improve the

13 quality of life of patients in the course of both

14 our Phase 2 and Phase 3 studies.

15 [Slide.]

16 I would now like to move to the

17 pharmacodynamics. Both Dr. Bonvini and Dr. Adelman

18 have elegantly described the mechanism of action to

19 you. I now want to review the range of alefacept-mediated

20 lymphocyte effects that we documented in

21 Phases II and III.

22 To do that, I will focus specifically on

23 the Phase 3 IV study, the two-course study. We

24 have similar data from the Phase 2 study and also

25 the Phase 3 IM study. These were summarized in

54

1 your briefing documents.

2 [Slide.]

3 I will consider both the mean counts over

4 time to convey the range of qualitative changes

5 that we can expect to see and also convey the

6 individual patient experience because there are

7 data of clinical relevance that we should discuss.

8 Finally, I will close with a discussion of

9 the potential implications of the types of changes

10 we have seen with a specific question as to what

11 are the role of memory T-cells given that they are

12 targeted selectively by the agent. After doing

13 that, I want to consider what data do we have that

14 addresses does Biogen have evidence for integrity

15 of immune function in alefacept-treated patients.

16 [Slide.]

17 Here you see a diagram which is just a

18 variant of one that Dr. Adelman showed you earlier.

19 These are the major lymphocyte subpopulations in

20 our peripheral blood and lymphoid tissues. They

21 are dominated by two species, the CD4 and CD8 T-cell. The

22 CD4 T-cells are of two types. They are

23 either naive or they are memory.

24 CD8 T-cells, again, are of the same two

25 types, CD8 naive or CD8 memory. You will see data

55

1 demonstrating that alefacept selectively targets

2 CD4 and CD8 memory T-cells. From this diagram, you

3 can see that a reduction in CD4 or CD8 memory T-cells would

4 result in a reduction in the total CD4

5 T-cell count or a reduction of the total CD8 T-cell

6 count.

7 Those reductions, in turn, would summate

8 to result in a reduction of the total lymphocyte

9 count which can be easily assayed by the CBC.

10 [Slide.]

11 With that background, let me begin to

12 demonstrate the range of features. This graph

13 summarizes what is at the core of the program, the

14 selective effect of alefacept against memory T-cells. On

15 the left, you see the effect on CD4

16 memory T-cells, on the right, the effect on naive

17 T-cells. It is immediately apparent that, in the

18 memory compartment, there is no significant effect

19 in the placebo group but, in the Phase 3 IV study,

20 the dosing period was associated with a reduction

21 in counts during the dosing interval.

22 Contrasting that to the findings on the

23 right, you see no significant changes in the naive

24 CD4 T-cells in either the placebo or the alefacept-treated

25 patients. We have identical data for the

56

1 CD8 memory and naive T-cells.

2 [Slide.]

3 Taking the CD4 memory T-cells a step

4 further, changes in this compartment would result

5 in a change in CD4 memory T-cells as a whole.

6 Those changes are illustrated here. You can see,

7 on the dotted line, no significant changes in the

8 placebo group during dose and a significant

9 reduction in alefacept during the dosing interval

10 with an increasing count following withdrawal of

11 treatment.

12 At all timepoints, just as we saw for

13 total lymphocyte counts, the mean, and I emphasize

14 the mean, CD4 T-cell count, remains above the low

15 limit of normal.

16 [Slide.]

17 Finally, the total lymphocyte count; you

18 can see, again, in placebo, no significant changes.

19 In alefacept, significant reduction during dosing

20 and increasing counts upon withdrawal of therapy.

21 Again, the mean counts remain above the low limit

22 of normal.

23 So that is one course of therapy. Cohort

24 1 in the Phase 3 IV study had two courses of

25 therapy.

57

1 [Slide.]

2 The mean CD4 T-cell changes for that

3 cohort are illustrated on this graph. On the left,

4 you see the Course 1 data. On the right, you see

5 the Course 2 data for the same patients. There are

6 three features in common that I want to go through

7 here. Number one, the rate of change during the

8 dosing interval is identical between Courses 1 and

9 2.

10 Number 2, the nadir reach for mean counts

11 is identical between Courses 1 and 2. Finally, the

12 rate of increase following withdrawal of therapy is

13 also identical between Courses 1 and 2. Note that

14 while patients are on alefacept therapy when drug

15 is withdrawn, they haven't, as yet, reached

16 baseline. At all timepoints, patients maintain

17 mean counts above the low limit of normal.

18 [Slide.]

19 Contrasting those ranges of features

20 considering the entire treatment groups and

21 starting to look at individual patients, we can see

22 the range of effects. To do the most conservative

23 analysis, what we illustrate here are the patients

24 that experienced total lymphocyte in the first row,

25 CD4 in the second row and CD8 in the third row.

58

1 Counts below the lower limit of normal at any time

2 point during the course of the Phase 3 IV studies

3 either in Course 1 or in Course 2. These are the

4 same patients dosed in both intervals.

5 This is a conservative approach because we

6 count patients, even if they went below normal just

7 on one occasion and came back. Given that most

8 individual's counts are very volatile, this is

9 probably an overestimate of the data. But it is

10 important we go through these carefully.

11 For total lymphocyte counts, the

12 proportions that went below normal in the first

13 course were 18 percent in the first course and 17

14 percent in the second. The CD4 T-cell count, the

15 proportions below normal, first course 44, second

16 course 44. For CD8 T-cell count, 51 percent in the

17 first course and a suggestion of incremental events

18 with 56 percent in the second course.

19 [Slide.]

20 If patients go below normal, then how did

21 they achieve counts within the normal range. I

22 have illustrated that here by looking at patients

23 who achieve counts to within the normal range after

24 twelve injections of IV therapy. These are data

25 from the Cohort 2 in the Phase 3 IV study whom, you

59

1 will recall, have twelve weeks of treatment and

2 then we followed for a 36-week period off drug.

3 That 36-week interval is the time course on this X-axis.

4 The Y-axis illustrates the proportions who

5 achieve counts within the normal range.

6 Immediately after the twelve injections, you can

7 see 63 percent of patients have counts within the

8 normal range. As we follow patients out, you can

9 see that, by Day 180, 90 percent of patients have

10 achieved a count within the normal range.

11 Finally, as we look at the last time

12 point, it appears that there are patients who are

13 missing while these are patients, 16 patients, who,

14 almost in all cases, were lost to follow up. Some

15 of these patients at the last point of observation

16 had counts between 300 to 400, but they disappeared

17 at any time during this interval and, for purposes

18 of summary, we just leave them missing here.

19 [Slide.]

20 The range of alefacept effects, I have

21 just described, are based upon careful monitoring.

22 In the Phase 3 studies, dosing was only initiated

23 in those with CD4 T-cell counts in the normal

24 range. Dose admission was carried out with

60

1 substitution of placebo for those patients that had

2 a CD4 T-cell count under 250 recalling that the low

3 limit of normal is 404 cells per microliter.

4 Finally, moving forwards, despite the fact

5 that we have not found any evidence of

6 immunodeficiency associated with the lower T-cell

7 counts, we propose a conservative approach, CD4 T-cell

8 monitoring every two weeks during therapy.

9 [Slide.]

10 Having gone through the phenomenology of

11 the pharmacodynamic effects, I now want to discuss

12 what are the potential implications for us as

13 clinicians here. That depends on a question what

14 are the actual functions of the memory T-cells that

15 are being manipulated.

16 In the physiological setting, memory T-cell are

17 important in the prevention of infections.

18 They are important in assisting B-cells for

19 antibody responses to recall antigens so when we

20 get reexposure to an antigen we have previously

21 seen, the IgG responses are critically dependent on

22 memory help.

23 Finally, they play a potential role in

24 immune surveillance in conjunction with other cell

25 types such as natural killer cells. That is in the

61

1 physiological setting. In the pathological

2 setting, Dr. Adelman has already discussed data

3 demonstrating that memory T-cells are important in

4 the induction of a range of autoimmune disorders

5 including psoriasis.

6 Over the next two or three minutes, I want

7 to close by addressing what sets of data do we have

8 addressing each of these points.

9 [Slide.]

10 First, the issue of infections and T-cell

11 counts. In the randomized placebo-controlled

12 studies, we divided patients into those that had

13 counts below 250 versus those that had counts above

14 250 and quantified the patients that had infections

15 after counts under 250. That number was

16 24 percent. Contrasting that to those that had

17 infections when counts were above 250, 46 percent,

18 the data suggest that lower T-cell counts do not

19 predispose to infections. Now, this is a very

20 preliminary look at this dataset. My colleague,

21 Dr. Vigliani, who will discuss the safety profile

22 with you, will go into this topic further.

23 [Slide.]

24 We have carefully studied immune-function

25 tests in patients exposed to alefacept to try and

62

1 determine what evidence do we have for disturbance

2 of normal immunity. To do this, we have used both

3 cell-mediated--tested responses of cell-mediated

4 immunity and responses to humoral immunity. Cell-mediated

5 responses were most robustly addressed in

6 the Phase 2 part of the program, specifically in

7 the Phase 2 IV study that we discussed earlier, the

8 Ellis and Krueger study. There, delayed-type

9 hypersensitivity skin tests were carried out to a

10 range of skin antigens using a CMI multitest.

11 Minor trends towards loss of response to

12 some of the antigens was seen but, given the high

13 false-positive and false-negative rate as well as

14 the difficulty in conducting these types of

15 studies, there are some important caveats when we

16 review these data, and I would be happy to discuss

17 those with you.

18 Contrasting that to the humoral responses,

19 these were studied in the clinical study of 46

20 chronic-plaque-psoriasis patients of the type we

21 treated during Phase 3. They were given either

22 alefacept or placebo and immunized with two T-cell-dependent

23 antigens. These are antigens that T-cells are critically

24 involved in from mounting

25 antibody responses to as documented in a range of

63

1 immunodeficiency studies in the literature.

2 The antigens were phi-X-174, a neoantigen

3 that patients have never been exposed to where we

4 tested both response when they were naive to the

5 antigen as well as response after reexposure where

6 we are specifically testing memory function. We

7 also tested tetanus toxoid, an antigen that we are

8 all immunized to and we have preexisting immunity

9 to. Here the tetanus toxoid is a recall antigen

10 and we are testing the memory component.

11 When we did these studies, we found that

12 alefacept treatment did not abrogate anti-phi-X-174

13 or antitetanus antibody responses.

14 [Slide.]

15 To show you those data graphically, here

16 are the phi-X-174 responses over time. The X axis

17 is the dosing interval and follow up the Y axis is

18 the mean antibody titer in log units. The primary

19 exposure is associated with a brisk rise in

20 antibody titer in both the alefacept and control

21 groups which is overlapping. This demonstrates

22 that naive T-cell function is intact in the

23 alefacept-treated patients. They can respond to

24 neoantigens.

25 The reexposure or the secondary

64

1 immunization is associated with a brisk rise in

2 both groups again which appears to be entirely

3 overlapping. The proportion IgG fraction in these

4 patients receiving either alefacept or placebo was

5 identical demonstrating that alefacept patients

6 undergo changes in memory-T-cell counts but that

7 these do not result in a change in their ability to

8 mount antibody responses.

9 We have similar data where we demonstrated

10 that patients had a twofold rise in antibody titer

11 against tetanus toxoid that was identical between

12 both alefacept and control groups.

13 [Slide.]

14 Finally, I want to turn to the issue of

15 what about the pathological setting, given these

16 manipulations of discrete T-cell subsets, do we

17 have data validating the therapeutic rationale as

18 originally proposed by Dr. Adelman. Here we have

19 documented the response on CD4 memory T-cells and

20 to what extent that correlated with the likelihood

21 of patients achieving PASI 75.

22 Now, on the X-axis, you see this axis

23 graded low to high where patients are divided in

24 quartiles, where the reduction in CD4 memory T-cells is

25 divided into four groups. Those in the

65

1 first quartile of the lowest group had the least

2 CD4 memory T-cell changes. Those in the highest

3 quartile had the greatest extent of CD4 memory T-cell

4 changes. Those intermediate had intermediate

5 changes.

6 Now, as you go from left to right, you can

7 see the stepwise increase in the likelihood of

8 response to PASI 75; 13, 23, 33 and 41 percent.

9 These are encouraging data but they are somewhat

10 indirect because we are looking for the surrogate

11 whereas the site of action is really the skin

12 lesion.

13 [Slide.]

14 To address that, Jim Krueger has conducted

15 a study over the last eighteen months asking the

16 question what do we understand about changes in T-cells in

17 the skin and outcomes after a patient is

18 treated with alefacept. Here are just some of his

19 data. What you see here is a plot of the T-cell

20 number at various time points for 21 patients pre-clin

21 versus the change in epidermal thickness at

22 those corresponding time points when the T-cell

23 number was assayed.

24 You can see the data are tightly gathered.

25 In fact, the r-value is 0.87. This suggests a very

66

1 tight correlation between the change in T-cell

2 number in the skin associated with alefacept

3 therapy and the therapeutic outcome.

4 The last two slides provide important data

5 validating the therapeutic rationale as originally

6 proposed.

7 [Slide.]

8 So I would like to close my presentation

9 by summarizing that, for lymphocyte

10 pharmacodynamics, both in Phases 2 and 3, we have

11 demonstrated that alefacept treatment is associated

12 with selective reductions of memory T-cells with a

13 relative sparing of naive T-cells. There is a

14 great deal of more data behind that bullet point

15 and some of those are with Dr. Krueger from his

16 studies where he has also demonstrated selectivity

17 of changes in the skin versus blood with preference

18 towards changes in the skin and also changes in

19 discrete sub-subsets of memory cells, specifically

20 those that are home to skin to mediate the disease

21 versus those that reside in the central memory

22 compartments. We can, perhaps, review some of

23 those data in the Q&A.

24 With respect to the second point, we have

25 demonstrated dose-dependent and gradual and

67

1 predictable changes during therapy. The findings

2 are consistent and predictable throughout. There

3 has been an increase in lymphocyte counts following

4 cessation of therapy and the reductions in T-cell

5 counts that we have seen have been correlated with

6 efficacy as I demonstrated but have not predisposed

7 to infections.

8 That is a suitable point to turn to the

9 discussion of the safety profile and I will now ask

10 my colleague, Dr. Vigliani, to come up.

11 Before she comes up, there is just one

12 point I would like to address was the

13 pharmacokinetics which I didn't discuss. The

14 pharmacokinetics are very consistent for the IM and

15 IV and there is as minor point of clarification.

16 In one of the briefing documents, there were some

17 placebo patients that were said to have alefacept

18 in their circulation during the PK assays. Those

19 patients have been revisited and we have provided

20 data to the FDA that have resolved that,

21 demonstrating that this was inference in the assay

22 at baseline. Those were false positives.

23 So, with that, Dr. Vigliani, if you could--

24 DR. DRAKE: I would like to take the

68

1 prerogative of the chair. I have looked at your

2 slides and the time left. So I just want us to the

3 cognizant of your allotted time. We are a little

4 bit--I don't know how you have divvied it up among

5 yourselves, but if we could try to hold--the next

6 two presenters please hold to the time schedule, we

7 would be appreciative.

8 Thank you.

9 DR. VAISHNAW: Okay.

10 Clinical Safety

11 DR. VIGLIANI: Good morning.

12 [Slide.]

13 It is my pleasure to be here today to

14 deliver the clinical-safety presentation.

15 [Slide.]

16 I will begin by defining the size and

17 scope of the clinical-safety database. I will then

18 review the most common and most serious adverse

19 events. I will review all deaths and will then

20 focus on the issue of malignancy and infection

21 since these are important areas of interest with

22 any new immunomodulatory therapy. Finally, since

23 alefacept is a protein immunobiologic, I will

24 discuss the issue of immungenicity.

25 [Slide.]

69

1 Let's now turn to the clinical-safety

2 database. Within clinical-safety database are the

3 876 patients from the three placebo-controlled

4 studies previously discussed. We have integrated

5 the data from these three studies and done pooled

6 analyses comparing event rates in alefacept-treated

7 patients with event rates in placebo-treated

8 patients.

9 The integrated analysis provides larger

10 numbers of patients thereby increasing sensitivity

11 for detection of trends not observed in individual

12 studies. However, important differences by study

13 occurring in the individual studies will be

14 highlighted when relevant.

15 The total clinical experience that we are

16 discussing today consists of 1157 chronic-plaque-psoriasis

17 patients from all alefacept studies in

18 which patients have received between one and five

19 courses of treatment. The comparisons presented

20 today will include the integrated placebo-controlled patient

21 experience as well as the

22 experience by course.

23 [Slide.]

24 When reviewing the placebo-controlled

25 comparisons, keep in mind that there is significant

70

1 disparity in terms of the number of patients

2 receiving alefacept and the number of patients

3 receiving placebo. If we compare the patient years

4 of exposure, as shown on the Y-axis, you can see

5 that alefacept exposure is more than two times that

6 of placebo exposure.

7 The person-year exposure is further

8 magnified when considering the total alefacept

9 people database. The higher person-year exposure

10 in alefacept-treated patients increases the

11 likelihood of capturing adverse events in these

12 patients. Additionally, events of low frequency

13 have an even lower likelihood of being observed in

14 the placebo group.

15 [Slide.]

16 Let us now move to a broad safety overview

17 of the placebo-controlled studies examining four

18 categories of events; incidence of any adverse

19 events, serious adverse events, discontinuations

20 due to adverse events and deaths. Here we find

21 that both alefacept and placebo groups are well

22 balanced in each of the categories. There was one

23 death in the alefacept group, a patient who

24 committed suicide related to his long-standing skin

25 disease.

71

1 [Slide.]

2 The safety overview by course provides a

3 similar picture. If you look across the top of

4 this table, you can see the number of patients

5 exposed during each course. Upon review of the

6 four categories, there is no broad evidence of

7 cumulative toxicity based upon this top-level view

8 of these important categories of events.

9 [Slide.]

10 If we now take a look at the most

11 frequently observed adverse events, that is those

12 seen at greater than or equal to 5 percent

13 incidence in placebo-controlled studies, we see

14 that 79 versus 83 percent experienced adverse

15 events. The range of adverse events reported is

16 typical for the population studied. There are no

17 unusual or atypical events.

18 You can see that none of the adverse

19 events occurred at a rate of 20 percent or greater.

20 This speaks to the overall tolerability of

21 alefacept and also speaks to investigators' ability

22 to maintain the integrity of the blind during these

23 studies.

24 When you compare the left-hand column to

25 the right-hand column, you can see that the groups

72

1 are generally well-balanced. When we look at

2 differences on the order of 5 percent or greater,

3 we find only one event, chills, occurring in 1

4 percent of the placebo group and in 6 percent of

5 the alefacept group. This is the one adverse event

6 that has consistently been associated with

7 alefacept exposure.

8 Chills were generally seen via the

9 intravenous route of administration, were generally

10 mild occurring early in the course of therapy and

11 were not associated with fever or other symptoms

12 and, importantly, did not result in discontinuation

13 of study drug.

14 One category of adverse events not listed

15 on this slide is injection-site reactions because

16 they occurred at an overall incidence of less than

17 5 percent in the integrated database. They did,

18 however, occur at a higher rate in the

19 intramuscular Phase 3 study. However, they did not

20 represent a significant tolerability issue.

21 [Slide.]

22 I would like to now consider serious

23 adverse events. These events were largely

24 considered serious based upon the regulatory

25 serious based upon the regulatory definition of

73

1 serious and, in most cases, this was based upon the

2 requirement for hospitalization.

3 [Slide.]

4 This table displays serious adverse events

5 seen in more than one alefacept-treated patient in

6 the placebo-controlled experience. The complete

7 table can be found in your briefing document.

8 Alefacept and placebo were well-balanced with 5

9 percent incidence of serious adverse events in each

10 group.

11 The most frequently observed event was

12 psoriasis which occurred in six patients in the

13 placebo group and in two patients in the alefacept

14 group. Serious adverse events observed both in

15 alefacept and placebo included chest pain and

16 pancreatitis. Some events show a slight imbalance

17 with higher rates in alefacept-treated patients--for

18 example, coronary-artery disorder, cellulitis

19 and myocardial infarction.

20 This apparent imbalance may be explained,

21 at least in part, by the fact that we have much

22 greater alefacept exposure than placebo exposure

23 and the number of events is small. Also note that

24 numerous single occurrences of serious adverse

25 events are not displayed in this partial table

74

1 accounting for the similar overall rates of serious

2 adverse events between the two groups.

3 [Slide.]

4 The rates of serious adverse events did

5 not increase with increased exposure in repeated

6 courses. So if you look along the top in yellow, 5

7 percent in the first course and going down to 2

8 percent in the fifth course experience serious

9 adverse events.

10 The range of adverse events seen were,

11 again, typical for the population studied and

12 didn't change significantly from those observed in

13 the placebo-controlled studies. Considering some

14 of the individual events noted at a higher rate in

15 the placebo-controlled experience such as coronary-artery

16 disease and cellulitis, none increased in

17 incidence with further courses of therapy.

18 Importantly, when evaluating overall

19 observed rates for events such as myocardial

20 infarction and coronary -artery disease, the rates

21 are consistent with the expected rates in the

22 general population based upon available

23 epidemiological data.

24 [Slide.]

25 I will now review the reported deaths

75

1 within the program. There have been a total six

2 deaths in the alefacept program to date. The first

3 four were detailed in your briefing document.

4 Three of these occurred in patients on alefacept

5 and one patient died prior to receiving study drug.

6 Two additional deaths have been reported

7 since the briefing document and are listed below

8 the line at the bottom of this table. Moving to

9 the top of this slide, we see the suicide

10 previously mentioned. This involved a 34-year-old

11 man with a lifelong history of psoriasis and,

12 unfortunately, a family history of suicide. His

13 disease was featured prominently in his suicide

14 note.

15 This case clearly illustrates the

16 psychosocial impact that psoriasis has in this

17 patient population. There were two deaths from

18 myocardial infarction. Both were middle-aged men

19 with multiple risk factors. While one occurred in

20 a patient on alefacept, the other occurred prior to

21 receipt of study drug.

22 These cases emphasize some of the

23 comorbidities in the study population. The fourth

24 patient died because of esophageal carcinoma

25 resulting from Barrett's esophagus. The two

76

1 remaining deaths reported after your briefing

2 document include a case of lung carcinoma in a

3 heavy smoker and a patient with a history of

4 seizures who died during a grand mal seizure in his

5 sleep ten months after receiving study drug.

6 [Slide.]

7 Let's now move to a discussion of

8 infections. In addition to collecting adverse

9 events, investigators were required to perform an

10 assessment of the patient for signs and symptoms

11 and infection at each study visit. They were

12 further required to record whether each adverse

13 event represented a new or ongoing infection.

14 Now, this prospective collection of

15 adverse events associated with infection

16 facilitated the identification and analysis of

17 these events. We have also analyzed the risk of

18 infection in relation to reductions in T-cell

19 counts.

20 [Slide.]

21 Looking first at infections that occurred

22 at an incidence of 5 percent or greater in the

23 placebo-controlled studies, 43 versus 45 percent in

24 the two groups experienced an event associated with

25 infection. There were only four events that

77

1 occurred at an incidence of greater than or equal

2 to 5 percent. These include pharyngitis,

3 nasopharyngitis or the common cold, flu-like

4 symptoms and nonspecific viral infection.

5 As you compare placebo to alefacept for

6 these four events, note that the groups are well-balanced

7 leading to the conclusion that alefacept

8 did not predispose to these common types of

9 infections.

10 [Slide.]

11 Now let's look at whether any of these

12 infections occurred at a higher rate in patients

13 with low CD4 counts. During the pharmacodynamic

14 part of the presentation, Dr. Vaishnaw showed you

15 the top part of this table in yellow. Note that a

16 lower proportion, or 24 percent of patients who had

17 CD4 counts less than 250 developed an infection

18 compared with 46 percent of those who maintained

19 counts above 250.

20 The rest of this table illustrates the

21 range of infections that were associated with low

22 T-cell counts. As you scan through the events,

23 note that there are no events suggestive of

24 opportunistic infections or immunodeficiency. If

25 you compare the incidences for these infections by

78

1 the CD4-count groupings, you see no significant

2 imbalance.

3 We have analyzed rates of infections for

4 different CD4 thresholds as well as CD8 thresholds

5 and have found no correlation between the risk of

6 infection or serious infection and reduction in

7 lymphocyte counts. The same holds true if you look

8 at data from the multiple course experience. This

9 leads to the conclusion that alefacept-mediated

10 reductions in lymphocyte counts do not predispose

11 to infection.

12 [Slide.]

13 Now let's turn our attention to serious

14 infections. Serious infections were observed at an

15 equal rate of less than 1 percent in both alefacept

16 and placebo groups. There were no atypical or

17 opportunistic infections. This is the placebo-controlled

18 experience. The data are similar across

19 the multicourse experience as described in your

20 briefing document. There were a total of 19

21 serious infections in the entire alefacept

22 database. You may notice that skin infections were

23 the most frequent category of infection in the

24 placebo-controlled experience. Therefore, we will

25 now look at this issue in greater depth focussing

79

1 on all serious skin infections in the entire 1300-patient

2 database.

3 [Slide.]

4 This table displays the case details of

5 all serious skin infections across the entire

6 program. These are divided into skin infections

7 and postoperative wound infections. Note that in

8 almost all of the cases, there were significant

9 risk factors which alone could account for the

10 types of infections observed.

11 For example, several patients had diabetes

12 mellitus and/or a disruption of the integrity of

13 the normal skin barrier. The first patient, a

14 diabetic, had a history of recurrent otitis

15 externa. The second had manipulated a sty with

16 resultant pre-septal cellulitis. The third had

17 multiple cardiopulmonary medical problems and was

18 treated for a presumed cellulitis, complicating

19 peripheral edema and erythema surrounding a large

20 psoriatic plaque.

21 Another patient with a history of

22 arthritis had a small finger abscess following

23 treatment of olecranon bursitis five months after

24 study drug. Another developed cellulitis

25 surrounding a Herpes simplex lesion near the eye.

80

1 Each of these patients had uncomplicated

2 infections and responded to conventional therapy.

3 Additionally, there was one case of cellulitis

4 resulting from a large burn and a case of toxic-shock

5 syndrome occurring two months after

6 completing alefacept. This patient experienced the

7 usual complications of toxic-shock syndrome but

8 made a full recovery.

9 In addition, three postoperative wound

10 infections were reported, one requiring

11 debridement, repeated debridement after a rotator-cuff

12 repair. This patient has since continued in

13 retreatment studies without further incident.

14 The two others included a repair of an

15 open and lacerated fracture of the tibia and a

16 surgical infection following appendiceal rupture.

17 Note also that more than 50 percent

18 underwent surgical procedures without such

19 complications. In all cases, patients were treated

20 with conventional therapies will full recovery.

21 The majority of patients continued with treatment.

22 There was no correlation between serious infection

23 and reduction in CD4 counts.

24 I would like to take a minute to discuss

25 the burn infection in greater depth as I feel that

81

1 it illustrates that maintenance of normal immune

2 function almost certainly contributed to a

3 favorable outcome in a high-risk patient. The

4 patient was an obese diabetic man who dropped a hot

5 radiator on his abdomen while maintaining his car

6 sustaining a large abdominal burn measuring 18 by

7 24 centimeters.

8 Despite a significant disruption in the

9 normal protective skin barrier in an area where

10 wound healing would be otherwise compromised, this

11 patient had an uncomplicated and brief admission to

12 the hospital responding to a course of conventional

13 antibiotics and topical treatments of his burn.

14 [Slide.]

15 So, with regard to infections, we can make

16 the following conclusions. The incidence and

17 nature of infections observed were similar between

18 alefacept and placebo. Low CD4 counts did not

19 appear to predispose to infections. There was no

20 evidence of increasing risk of infections by

21 course. The serious infections observed were

22 uncomplicated in nature, clinical course and

23 outcome.

24 Most importantly, we observed no

25 opportunistic infections, no tuberculosis and no

82

1 deaths due to infection. Finally, there was no

2 indication that the types of infections that would

3 be suggestive of a T-cell immunodeficiency were

4 observed in the association with alefacept therapy.

5 [Slide.]

6 So we have asked ourselves the question

7 why is it that we haven't seen an increase in the

8 risk of infection despite the significant T-cell

9 effects of this drug. There are a number of

10 possible reasons for this observation.

11 The first is that alefacept does not alter

12 naive T-cells allowing patients to respond normally

13 to new bacterial, viral and other antigens. The

14 second is that the effect of alefacept against

15 memory T-cells is only partial. The remaining T-cells

16 appear to be sufficient to promote antibody

17 responses as demonstrated in the immune-function

18 study previously discussed.

19 Third, there is significant redundancy

20 within the immune system with memory functions

21 divided between a number of important subsets that

22 include CD45RA-positive cells. We have also noted

23 that patients with infection are able to mount

24 increases in their lymphocyte counts. Given that

25 only 3 percent of the T-cell pool resides in the

83

1 circulation with the rest residing in lymph-node

2 tissue, maintenance of lymph-node integrity may

3 also explain why T-cell function appears to be

4 preserved.

5 [Slide.]

6 I will now turn to the topic of

7 malignancy.

8 [Slide.]

9 The proportion of patients with a

10 malignancy in placebo-controlled studies were less

11 than 1 percent for placebo and 1 percent for

12 alefacept. As expected in this population, the

13 most common cancer was non-melanoma skin cancer.

14 This categorization includes both squamous-cell

15 carcinoma and basal-cell carcinoma.

16 One patient in the placebo and six

17 patients in the alefacept group, less than 1

18 percent in each case, had skin cancers reported

19 during these studies. Two events of carcinoma,

20 both in the alefacept group, were cases of

21 testicular cancer and renal-cell carcinoma.

22 The patient with renal-cell cancer was

23 diagnosed with an 11-centimeter renal mass within

24 three weeks of initiation of therapy making

25 causality unlikely in that case. Prostate cancer